THIAMIN-RESPONSIVE MAPLE-SYRUP-URINE DISEASE - DECREASED AFFINITY OF THE MUTANT BRANCHED-CHAIN ALPHA-KETO ACID DEHYDROGENASE FOR ALPHA-KETOISOVALERATE AND THIAMIN PYROPHOSPHATE

被引：33
作者：
CHUANG, DT [1 ]
KU, LS [1 ]
COX, RP [1 ]
机构：
[1] CASE WESTERN RESERVE UNIV,CLEVELAND,OH 44106
来源：
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES | 1982年 / 79卷 / 10期
关键词：
D O I：
10.1073/pnas.79.10.3300
中图分类号：
Q [生物科学];
学科分类号：
07 ; 0710 ; 09 ;
摘要：
引用
收藏
页码：3300 / 3304
页数：5
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