CYLINDRICAL SPIRALS IN HUMAN SKELETAL-MUSCLE

被引:26
作者
CARPENTER, S
KARPATI, G
ROBITAILLE, Y
MELMED, C
机构
[1] MCGILL UNIV,MONTREAL NEUROL INST,DEPT PATHOL,MONTREAL H3A 2B4,QUEBEC,CANADA
[2] JEWISH GEN HOSP,MONTREAL H3T 1E2,QUEBEC,CANADA
关键词
D O I
10.1002/mus.880020407
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Muscle biopsies from two patients revealed that numerous type 2 fibers contained large abnormal areas filled with cylindrical spirals. The cytochemical profile of these cylindrical spirals was sufficiently characteristic that they could be distinguished from tubular aggregates. Their electron microscopic appearance was unmistakable. Their origin and significance are uncertain. The diverse nature of the patients' conditions (cramps and malignancy, and an unusual form of spinocerebellar degeneration) indicate that these abnormal structures are not disease specific. Copyright © 1979 Houghton Mifflin Professional Publishers
引用
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页码:282 / 287
页数:6
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