OVARIAN FIBROSARCOMA ASSOCIATED WITH MAFFUCCIS SYNDROME

被引:29
作者
CHRISTMAN, JE
BALLON, SC
机构
[1] DAVID GRANT USAF MED CTR, TRAVIS AFB, CA 94535 USA
[2] STANFORD UNIV, MED CTR, DEPT OBSTET & GYNECOL, STANFORD, CA 94305 USA
[3] STANFORD UNIV, MED CTR, DEPT GYNECOL & OBSTET, STANFORD, CA 94305 USA
关键词
D O I
10.1016/0090-8258(90)90350-T
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
Maffucci's syndrome, a congenital condition of generalized mesodermal dysplasia, is most often associated with multiple enchondromas and soft tissue hemangiomas or lymphangiomas. This case report describes the development of an unusual ovarian fibrosarcoma and subsequent ovarian adenofibroma in a young woman with the syndrome. The importance of aggressive surveillance in this and similar orthopedic syndromes is stressed. © 1990.
引用
收藏
页码:290 / 291
页数:2
相关论文
共 9 条
[1]  
KUZMA JF, 1948, ARCH PATHOL, V46, P74
[2]   MAFFUCCIS SYNDROME - FUNCTIONAL AND NEOPLASTIC SIGNIFICANCE - CASE REPORT AND REVIEW OF LITERATURE [J].
LEWIS, RJ ;
KETCHAM, AS .
JOURNAL OF BONE AND JOINT SURGERY-AMERICAN VOLUME, 1973, A 55 (07) :1465-1479
[3]   MAFFUCCIS SYNDROME - A MESENCHYMAL DYSPLASIA AND MULTIPLE TUMOR SYNDROME [J].
LOEWINGER, RJ ;
LICHTENSTEIN, JR ;
DODSON, WE ;
EISEN, AZ .
BRITISH JOURNAL OF DERMATOLOGY, 1977, 96 (03) :317-322
[4]  
PRAT J, 1981, CANCER-AM CANCER SOC, V47, P2663, DOI 10.1002/1097-0142(19810601)47:11<2663::AID-CNCR2820471124>3.0.CO
[5]  
2-V
[6]  
SCULLY RE, 1979, ATLAS TUMOR PATHOL, P312
[7]  
TALERMAN A, 1977, MESENCHYMAL TUMORS M, P562
[8]  
TAMIMI HK, 1984, CANCER, V53, P1605, DOI 10.1002/1097-0142(19840401)53:7<1605::AID-CNCR2820530731>3.0.CO
[9]  
2-N