MALIGNANT VENTRICULAR ARRHYTHMIA IN SYSTEMIC-SCLEROSIS CONTROLLED WITH AN IMPLANTABLE CARDIOVERTER-DEFIBRILLATOR

被引:0
作者
MARTINEZTABOADA, V
OLALLA, J
BLANCO, R
ARMONA, J
SUEIRO, JF
RODRIGUEZVALVERDE, V
机构
[1] UNIV CANTABRIA,HOSP UNIV M VALDECILLA,FAC MED,DIV RHEUMATOL,E-39008 SANTANDER,SPAIN
[2] UNIV CANTABRIA,HOSP UNIV M VALDECILLA,FAC MED,DIV CARDIOL,E-39008 SANTANDER,SPAIN
关键词
SYSTEMIC SCLEROSIS; VENTRICULAR ARRHYTHMIAS; IMPLANTABLE CARDIOVERTER DEFIBRILLATOR; ANTIARRHYTHMIC THERAPY;
D O I
暂无
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
The prognosis of systemic sclerosis (SSc) is poor, and a significant number of patients suffer sudden death, probably related to malignant ventricular arrhythmias for which there is no reliable drug treatment. We describe a patient with SSc who had 2 documented episodes of ventricular fibrillation, that reverted after electrical defibrillation. An electrophysiological study performed after 3 weeks of oral loading with amiodarone 1200 mg/day, demonstrated the induction of unstable sustained syncopal ventricular tachycardia. She has been successfully controlled with the implant of a 3rd generation implantable cardioverter defibrillator. We suggest that this treatment should be seriously considered in those patients with SSc and malignant ventricular arrhythmias unresponsive to drug therapy.
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页码:2166 / 2167
页数:2
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