EFFECT OF CYSTINE DIMETHYLESTER ON RENAL SOLUTE HANDLING AND ISOLATED RENAL TUBULE TRANSPORT IN THE RAT - A NEW MODEL OF THE FANCONI SYNDROME

被引:41
作者
FOREMAN, JW
BOWRING, MA
LEE, J
STATES, B
SEGAL, S
机构
[1] CHILDRENS HOSP,DIV BIOCHEM DEV & MOLEC DIS,34TH & CIVIC CTR BLVD,PHILADELPHIA,PA 19104
[2] UNIV PENN,SCH MED,DEPT PEDIAT,PHILADELPHIA,PA 19104
[3] UNIV PENN,SCH MED,DEPT MED,PHILADELPHIA,PA 19104
来源
METABOLISM-CLINICAL AND EXPERIMENTAL | 1987年 / 36卷 / 12期
关键词
D O I
10.1016/0026-0495(87)90246-0
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:1185 / 1191
页数:7
相关论文
共 25 条
[1]   CELLULAR ACCUMULATION OF L-LYSINE IN RAT-KIDNEY CORTEX IN-VIVO [J].
AUSIELLO, DA ;
THIER, SO ;
SEGAL, S .
AMERICAN JOURNAL OF PHYSIOLOGY, 1972, 222 (06) :1473-&
[2]   OXYGEN CONSUMPTION AND ACTIVE TRANSPORT IN SEPARATED RENAL TUBULES [J].
BURG, MB ;
ORLOFF, J .
AMERICAN JOURNAL OF PHYSIOLOGY, 1962, 203 (02) :327-&
[3]   DEVELOPMENTAL ASPECTS OF RENAL BETA-AMINO ACID TRANSPORT .1. ONTOGENY OF TAURINE REABSORPTION AND ACCUMULATION IN RAT RENAL CORTEX [J].
CHESNEY, RW ;
JAX, DK .
PEDIATRIC RESEARCH, 1979, 13 (07) :854-860
[4]  
CHESNEY RW, 1979, RENAL PHYSL, V1, P166
[5]   INTRACELLULAR RATIO OF CYSTEINE AND CYSTINE IN VARIOUS TISSUES [J].
CRAWHALL, JC ;
SEGAL, S .
BIOCHEMICAL JOURNAL, 1967, 105 (02) :891-&
[6]   TRANSPORT INTERACTIONS OF CYSTINE AND DIBASIC AMINO-ACIDS IN ISOLATED RAT RENAL TUBULES [J].
FOREMAN, JW ;
HWANG, SM ;
SEGAL, S .
METABOLISM-CLINICAL AND EXPERIMENTAL, 1980, 29 (01) :53-61
[7]   CHARACTERISTICS OF CYSTINE COUNTER-TRANSPORT IN NORMAL AND CYSTINOTIC LYSOSOME-RICH LEUKOCYTE GRANULAR FRACTIONS [J].
GAHL, WA ;
TIETZE, F ;
BASHAN, N ;
BERNARDINI, I ;
RAIFORD, D ;
SCHULMAN, JD .
BIOCHEMICAL JOURNAL, 1983, 216 (02) :393-400
[8]  
GAHL WA, 1982, J BIOL CHEM, V257, P9570
[9]  
GOLDENBERG H, 1966, CLIN CHEM, V12, P871
[10]   RUPTURE OF RAT-LIVER LYSOSOMES MEDIATED BY L-AMINO-ACID ESTERS [J].
GOLDMAN, R ;
KAPLAN, A .
BIOCHIMICA ET BIOPHYSICA ACTA, 1973, 318 (02) :205-216