UNCOMMON CLINICAL PRESENTATION OF A LYMPHOCYTIC LYMPHOMA OF INTERMEDIATE DIFFERENTIATION IN A PATIENT WITH SYSTEMIC-SCLEROSIS

被引:9
作者
BALDINI, L
GUFFANTI, A
FERRARI, A
CASTAGNONE, D
MASCAGNI, B
FRACCHIOLLA, N
COLOMBI, M
MAIOLO, AT
机构
[1] UNIV MILAN,OSPED MAGGIORE,IRCCS,SERV RADIOL 2,MILAN,ITALY
[2] UNIV MILAN,OSPED MAGGIORE,IRCCS,IST MED INTERNA & IMMUNOPATOL,MILAN,ITALY
[3] OSPED FATEBENEFRATELLI & OFTALMICO,DIV MED 1,MILAN,ITALY
[4] OSPED FATEBENEFRATELLI & OFTALMICO,SERV ANAT PATOL,MILAN,ITALY
关键词
SYSTEMIC SCLEROSIS; LYMPHOCYTIC LYMPHOMA OF INTERMEDIATE DIFFERENTIATION; MANTLE-ZONE LYMPHOMAS;
D O I
10.1111/j.1365-2141.1994.tb04803.x
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
The association of systemic sclerosis (SSc) and non-Hodgkin lymphoma is a rare event and its pathogenetic mechanism remains to be clarified. We describe a previously unreported association of SSc with a lymphocytic lymphoma of intermediate differentiation (IDL), involving the gastrointestinal tract, gallbladder and one salivary gland. Whereas the morphological, immunological and cytogenetic features were typical of IDL, the extensive extranodal involvement and the association with an autoimmune disorder were suggestive of two other lymphomas of mantle lineage: mucosa-associated lymphoid tissue (MALT) lymphoma and monocytoid B-cell lymphoma (MBCL).
引用
收藏
页码:657 / 658
页数:2
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