ALVEOLAR HEMORRHAGE WITH EPITHELIOID HEMANGIOENDOTHELIOMA - A PREVIOUSLY UNREPORTED MANIFESTATION OF A RARE TUMOR

被引:25
作者
CARTER, EJ [1 ]
BRADBURNE, RM [1 ]
JHUNG, JW [1 ]
ETTENSOHN, DB [1 ]
机构
[1] BROWN UNIV,MEM HOSP RHODE ISL,DEPT MED,DIV PULM MED,PROGRAM MED,PROVIDENCE,RI 02912
来源
AMERICAN REVIEW OF RESPIRATORY DISEASE | 1990年 / 142卷 / 03期
关键词
D O I
10.1164/ajrccm/142.3.700
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
Epithelial hemangioendothelioma (EH), originally termed intravascular sclerosing bronchioloalveolar tumor (IVBAT), is a rare pulmonary vascular neoplasm usually associated with an indolent but slowly progressive clinical course. We describe a patient with EH who presented with alveolar hemorrhage and died within 8 wk. This report extends the clinical spectrum of epithelial hemangioendothelioma to include this aggressive form. EH should be considered in the differential diagnosis of alveolar hemorrhage syndrome.
引用
收藏
页码:700 / 701
页数:2
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