ENZYMATIC DEFECT IN VARIEGATE PORPHYRIA - STUDIES WITH HUMAN CULTURED SKIN FIBROBLASTS

被引：158

作者：

BRENNER, DA ^{[1
]}

BLOOMER, JR ^{[1
]}

机构：

[1] YALE UNIV,SCH MED,HOWARD HUGHES MED INST LAB,NEW HAVEN,CT 06520

来源：

NEW ENGLAND JOURNAL OF MEDICINE | 1980年 / 302卷 / 14期

关键词：

D O I：

10.1056/NEJM198004033021401

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

引用

页码：765 / 769

页数：5

共 26 条

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[2]

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BRENNER, DA ;

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[4]

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BONKOWSKY, HL ;

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[6]

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[7] FLUOROMETRIC ASSAY FOR MEASUREMENT OF PROTOPORPHYRINOGEN OXIDASE ACTIVITY IN MAMMALIAN TISSUE [J].

BRENNER, DA ;

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CLINICA CHIMICA ACTA, 1980, 100 (03) :259-266

[8]

BRODIE MJ, 1977, LANCET, V2, P699

[9]

ELDER GH, 1976, LANCET, V2, P1217

[10] RED-CELL UROPORPHYRINOGEN DECARBOXYLASE ACTIVITY IN PORPHYRIA CUTANEA-TARDA AND IN OTHER FORMS OF PORPHYRIA [J].

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