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GLOBOID CELL LEUCODYSTROPHY (KRABBES DISEASE) - DEFICIENCY OF GALACTOCEREBROSIDE BETA-GALACTOSIDASE
被引:463
作者
:
SUZUKI, K
论文数:
0
引用数:
0
h-index:
0
SUZUKI, K
SUZUKI, Y
论文数:
0
引用数:
0
h-index:
0
SUZUKI, Y
机构
:
来源
:
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
|
1970年
/ 66卷
/ 02期
关键词
:
D O I
:
10.1073/pnas.66.2.302
中图分类号
:
O [数理科学和化学];
P [天文学、地球科学];
Q [生物科学];
N [自然科学总论];
学科分类号
:
07 ;
0710 ;
09 ;
摘要
:
引用
收藏
页码:302 / &
相关论文
共 20 条
[1]
STUDIES IN GLOBOID (KRABBE) LEUKODYSTROPHY .1. SIGNIFICANCE OF LIPID ABNORMALITIES IN WHITE MATTER IN 8 GLOBOID AND 13 CONTROL PATIENTS
[J].
AUSTIN, J
论文数:
0
引用数:
0
h-index:
0
AUSTIN, J
.
ARCHIVES OF NEUROLOGY,
1963,
9
(03)
:207
-+
[2]
STUDIES IN GLOBOID (KRABBE) LEUKODYSTROPHY .3. SIGNIFICANCE OF EXPERIMENTALLY-PRODUCED GLOBOID-LIKE ELEMENTS IN RAT WHITE MATTER AND SPLEEN
[J].
AUSTIN, JH
论文数:
0
引用数:
0
h-index:
0
AUSTIN, JH
;
LEHFELDT, D
论文数:
0
引用数:
0
h-index:
0
LEHFELDT, D
.
JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY,
1965,
24
(02)
:265
-&
[3]
STUDIES IN GLOBOID (KRABBE) LEUKODYSTROPHY .2. CONTROLLED THIN-LAYER CHROMATOGRAPHIC STUDIES OF GLOBOID BODY FRACTIONS IN M PATIENTS
[J].
AUSTIN, JH
论文数:
0
引用数:
0
h-index:
0
AUSTIN, JH
.
JOURNAL OF NEUROCHEMISTRY,
1963,
10
(12)
:921
-&
[4]
BACHHAWAT BK, 1967, BIOCHEM J, V104, pC15
[5]
CEREBROSIDE GALACTOSIDASE - A METHOD FOR DETERMINATION AND A COMPARISON WITH OTHER LYSOSOMAL ENZYMES IN DEVELOPING RAT BRAIN
[J].
BOWEN, DM
论文数:
0
引用数:
0
h-index:
0
机构:
Mental Health Research Institute, University of Michigan, Ann Arbor, Michigan
BOWEN, DM
;
RADIN, NS
论文数:
0
引用数:
0
h-index:
0
机构:
Mental Health Research Institute, University of Michigan, Ann Arbor, Michigan
RADIN, NS
.
JOURNAL OF NEUROCHEMISTRY,
1969,
16
(04)
:501
-+
[6]
PURIFICATION OF CEREBROSIDE GALACTOSIDASE FROM RAT BRAIN
[J].
BOWEN, DM
论文数:
0
引用数:
0
h-index:
0
BOWEN, DM
;
RADIN, NS
论文数:
0
引用数:
0
h-index:
0
RADIN, NS
.
BIOCHIMICA ET BIOPHYSICA ACTA,
1968,
152
(03)
:587
-&
[7]
PROPERTIES OF CEREBROSIDE GALACTOSIDASE
[J].
BOWEN, DM
论文数:
0
引用数:
0
h-index:
0
BOWEN, DM
;
RADIN, NS
论文数:
0
引用数:
0
h-index:
0
RADIN, NS
.
BIOCHIMICA ET BIOPHYSICA ACTA,
1968,
152
(03)
:599
-&
[8]
KRABBES DISEASE - GLOBOID CELL TYPE OF LEUKODYSTROPHY
[J].
DAGOSTINO, AN
论文数:
0
引用数:
0
h-index:
0
DAGOSTINO, AN
;
SAYRE, GP
论文数:
0
引用数:
0
h-index:
0
SAYRE, GP
;
HAYLES, AB
论文数:
0
引用数:
0
h-index:
0
HAYLES, AB
.
ARCHIVES OF NEUROLOGY,
1963,
8
(01)
:82
-&
[9]
ETO Y, TO BE PUBLISHED
[10]
ISOLATION OF BETA-N-ACETYLHEXOSAMINIDASE BETA-N-ACETYLGLUCOSAMINIDASE AND BETA-N-ACETYLGALACTOSAMINIDASE FROM CALF BRAIN
[J].
FROHWEIN, YZ
论文数:
0
引用数:
0
h-index:
0
FROHWEIN, YZ
;
GATT, S
论文数:
0
引用数:
0
h-index:
0
GATT, S
.
BIOCHEMISTRY,
1967,
6
(09)
:2775
-&
←
1
2
→
共 20 条
[1]
STUDIES IN GLOBOID (KRABBE) LEUKODYSTROPHY .1. SIGNIFICANCE OF LIPID ABNORMALITIES IN WHITE MATTER IN 8 GLOBOID AND 13 CONTROL PATIENTS
[J].
AUSTIN, J
论文数:
0
引用数:
0
h-index:
0
AUSTIN, J
.
ARCHIVES OF NEUROLOGY,
1963,
9
(03)
:207
-+
[2]
STUDIES IN GLOBOID (KRABBE) LEUKODYSTROPHY .3. SIGNIFICANCE OF EXPERIMENTALLY-PRODUCED GLOBOID-LIKE ELEMENTS IN RAT WHITE MATTER AND SPLEEN
[J].
AUSTIN, JH
论文数:
0
引用数:
0
h-index:
0
AUSTIN, JH
;
LEHFELDT, D
论文数:
0
引用数:
0
h-index:
0
LEHFELDT, D
.
JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY,
1965,
24
(02)
:265
-&
[3]
STUDIES IN GLOBOID (KRABBE) LEUKODYSTROPHY .2. CONTROLLED THIN-LAYER CHROMATOGRAPHIC STUDIES OF GLOBOID BODY FRACTIONS IN M PATIENTS
[J].
AUSTIN, JH
论文数:
0
引用数:
0
h-index:
0
AUSTIN, JH
.
JOURNAL OF NEUROCHEMISTRY,
1963,
10
(12)
:921
-&
[4]
BACHHAWAT BK, 1967, BIOCHEM J, V104, pC15
[5]
CEREBROSIDE GALACTOSIDASE - A METHOD FOR DETERMINATION AND A COMPARISON WITH OTHER LYSOSOMAL ENZYMES IN DEVELOPING RAT BRAIN
[J].
BOWEN, DM
论文数:
0
引用数:
0
h-index:
0
机构:
Mental Health Research Institute, University of Michigan, Ann Arbor, Michigan
BOWEN, DM
;
RADIN, NS
论文数:
0
引用数:
0
h-index:
0
机构:
Mental Health Research Institute, University of Michigan, Ann Arbor, Michigan
RADIN, NS
.
JOURNAL OF NEUROCHEMISTRY,
1969,
16
(04)
:501
-+
[6]
PURIFICATION OF CEREBROSIDE GALACTOSIDASE FROM RAT BRAIN
[J].
BOWEN, DM
论文数:
0
引用数:
0
h-index:
0
BOWEN, DM
;
RADIN, NS
论文数:
0
引用数:
0
h-index:
0
RADIN, NS
.
BIOCHIMICA ET BIOPHYSICA ACTA,
1968,
152
(03)
:587
-&
[7]
PROPERTIES OF CEREBROSIDE GALACTOSIDASE
[J].
BOWEN, DM
论文数:
0
引用数:
0
h-index:
0
BOWEN, DM
;
RADIN, NS
论文数:
0
引用数:
0
h-index:
0
RADIN, NS
.
BIOCHIMICA ET BIOPHYSICA ACTA,
1968,
152
(03)
:599
-&
[8]
KRABBES DISEASE - GLOBOID CELL TYPE OF LEUKODYSTROPHY
[J].
DAGOSTINO, AN
论文数:
0
引用数:
0
h-index:
0
DAGOSTINO, AN
;
SAYRE, GP
论文数:
0
引用数:
0
h-index:
0
SAYRE, GP
;
HAYLES, AB
论文数:
0
引用数:
0
h-index:
0
HAYLES, AB
.
ARCHIVES OF NEUROLOGY,
1963,
8
(01)
:82
-&
[9]
ETO Y, TO BE PUBLISHED
[10]
ISOLATION OF BETA-N-ACETYLHEXOSAMINIDASE BETA-N-ACETYLGLUCOSAMINIDASE AND BETA-N-ACETYLGALACTOSAMINIDASE FROM CALF BRAIN
[J].
FROHWEIN, YZ
论文数:
0
引用数:
0
h-index:
0
FROHWEIN, YZ
;
GATT, S
论文数:
0
引用数:
0
h-index:
0
GATT, S
.
BIOCHEMISTRY,
1967,
6
(09)
:2775
-&
←
1
2
→