Congenital-Left Atrial Appendage Aneurysm in an 8-Year-Old Girl

Congenital aneurysm of the Left Atrial Appendage (LAA) is extremely rare because after the first case no was described by Diamond in 1960, only 50 cases have been reported in the literature. Congenital aneurysm of the LAA is rarely diagnosed during childhood. Generally it manifests during the second or third decades of life. We are reporting here a case of congenital left atrial appendage aneurysm in an 8 year old girl who presented with breathlessness on exertion which was present since 6 months. Pre-operatively, the diagnosis of aneurysm was made by chest radiography, echocardiography and magnetic resonance imaging. The surgical findings demonstrated a kidney shaped saccular aneurysm. The microscopic findings showed myocardial layers in variable numbers. Following an aneurysmectomy, the patient is now asymptomatic and in the sinus rhythm.