MICROVILLUS INCLUSION DISEASE - AN INHERITED DEFECT OF BRUSH-BORDER ASSEMBLY AND DIFFERENTIATION

被引:163
作者
CUTZ, E
RHOADS, JM
DRUMM, B
SHERMAN, PM
DURIE, PR
FORSTNER, GG
机构
[1] HOSP SICK CHILDREN,DEPT PAEDIAT,DIV GASTROENTEROL,555 UNIV AVE,TORONTO M5G 1X8,ONTARIO,CANADA
[2] HOSP SICK CHILDREN,DEPT PATHOL,TORONTO M5G 1X8,ONTARIO,CANADA
[3] UNIV TORONTO,TORONTO M5S 1A1,ONTARIO,CANADA
关键词
D O I
10.1056/NEJM198903093201006
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:646 / 651
页数:6
相关论文
共 23 条
[1]   BILE-ACID MALABSORPTION - CONSEQUENCE OF TERMINAL ILEAL DYSFUNCTION IN PROTRACTED DIARRHEA OF INFANCY [J].
BALISTRERI, WF ;
PARTIN, JC ;
SCHUBERT, WK .
JOURNAL OF PEDIATRICS, 1977, 90 (01) :21-28
[3]  
BOOTH IW, 1985, LANCET, V1, P1066
[4]  
CARRUTHERS L, 1986, CLIN GASTROENTEROL, V15, P105
[5]   BIOCHEMICAL-ABNORMALITY IN BRUSH-BORDER MEMBRANE-PROTEIN OF A PATIENT WITH CONGENITAL MICROVILLUS ATROPHY [J].
CARRUTHERS, L ;
PHILLIPS, AD ;
DOURMASHKIN, R ;
WALKERSMITH, JA .
JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION, 1985, 4 (06) :902-907
[6]  
CUTZ E, 1988, LAB INVEST, V58, pP3
[7]  
CUTZ E, 1986, LAB INVEST, V54, pP54
[8]   METHOD FOR ASSAY OF INTESTINAL DISACCHARIDASES [J].
DAHLQVIST, A .
ANALYTICAL BIOCHEMISTRY, 1964, 7 (01) :18-&
[9]  
DAVIDSON GP, 1978, GASTROENTEROLOGY, V75, P783
[10]  
DRUMM B, 1988, LANCET, V1, P111