BONE ANOMALIES IN MYOTONIC-DYSTROPHY

被引:12
作者
RODRIGUEZ, JR
CASTILLO, J
LEIRA, R
PARDO, J
LEMA, M
NOYA, M
机构
[1] Neurology Service, Galicia General Hospital, Santiago de Compostela University
来源
ACTA NEUROLOGICA SCANDINAVICA | 1991年 / 83卷 / 06期
关键词
MYOTONIC DYSTROPHY; HYPEROSTOSIS; BASAL GANGLIA CALCIFICATION;
D O I
10.1111/j.1600-0404.1991.tb03963.x
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Sixteen patients with myotonic dystrophy underwent CT examination of the skull, and measurement of bone mineral density at lumbar spine and hip by dual-photon absorptiometry. The results were compared with those of 20 normal subjects of similar age and sex distribution. Hyperostosis of the calvarium, and increased bone mineral density at lumbar vertebrae were observed. One case showed basal ganglia calcification associated with hyperparathyroidism secondary to deficiency of vitamin D. In the other 15 patients, studies of calcium metabolism were normal. There results suggest the existence of generalized hyperostotic potential in patients with myotonic dystrophy.
引用
收藏
页码:360 / 363
页数:4
相关论文
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