A FATAL CASE OF PORTAL-HYPERTENSION COMPLICATING SYSTEMIC MASTOCYTOSIS IN AN ADOLESCENT

被引：16
作者：
FONGADJIMI, HS [1 ]
GOTTRAND, F [1 ]
BONNEVALLE, M [1 ]
FARRIAUX, JP [1 ]
机构：
[1] HOP HURIEZ,SERV PEDIAT,F-59037 LILLE,FRANCE
来源：
EUROPEAN JOURNAL OF PEDIATRICS | 1995年 / 154卷 / 10期
关键词：
PORTAL HYPERTENSION; MASTOCYTOSIS; ADOLESCENT;
D O I：
10.1007/BF01959789
中图分类号：
R72 [儿科学];
学科分类号：
100202 ;
摘要：
Portal hypertension was observed in a 17-year-old girl with urticaria pigmentosa since 2 months of age. Liver biopsies showed portal and sinusoidal infiltration with mast cells although spleen biopsies showed only fibrosis. Conclusion Portal hypertension is a complication of systemic mastocytosis that can lead to death. Treatment with interferon alpha might be effective.
引用
收藏
页码：819 / 821
页数：3
相关论文
共 14 条
[1]   INTRACTABLE ASCITES IN SYSTEMIC MASTOCYTOSIS TREATED BY PORTAL DIVERSION [J].
BONNET, P ;
SMADJA, C ;
SZEKELY, AM ;
DELAGE, Y ;
CALMUS, Y ;
POUPON, R ;
FRANCO, D .
DIGESTIVE DISEASES AND SCIENCES, 1987, 32 (02) :209-213
[2]  
CAPRON JP, 1978, GASTROENTEROLOGY, V74, P595
[3]  
GHANDURMNAYMNEH L, 1985, ARCH PATHOL LAB MED, V109, P76
[4]  
GRUNDFEST S, 1980, GASTROENTEROLOGY, V78, P370
[5]   PEDIATRIC MASTOCYTOSIS [J].
KETTELHUT, BV ;
METCALFE, DD .
JOURNAL OF INVESTIGATIVE DERMATOLOGY, 1991, 96 (03) :S15-S18
[6]   RESPONSE TO INTERFERON-ALFA-2B IN A PATIENT WITH SYSTEMIC MASTOCYTOSIS [J].
KLUINNELEMANS, HC ;
JANSEN, JH ;
BREUKELMAN, H ;
WOLTHERS, BG ;
KLUIN, PM ;
KROON, HM ;
WILLEMZE, R .
NEW ENGLAND JOURNAL OF MEDICINE, 1992, 326 (09) :619-623
[7]   PORTAL-HYPERTENSION AND ASCITES IN SYSTEMIC MASTOCYTOSIS [J].
NARAYANAN, MN ;
YIN, JAL ;
AZZAWI, S ;
WARNES, TW ;
TURCK, WPG .
POSTGRADUATE MEDICAL JOURNAL, 1989, 65 (764) :394-396
[8]   LONG-TERM RESPONSE TO INTERFERON-ALPHA IN A PATIENT WITH SYSTEMIC MASTOCYTOSIS AND CHRONIC MYELOMONOCYTIC LEUKEMIA [J].
PULIK, M ;
LIONNET, F ;
PETIT, A ;
GENET, P ;
GAULIER, A .
AMERICAN JOURNAL OF HEMATOLOGY, 1994, 47 (01) :66-66
[9]   SYSTEMIC MASTOCYTOSIS, MYELOFIBROSIS AND PORTAL-HYPERTENSION [J].
SAWERS, AH ;
DAVSON, J ;
BRAGANZA, J ;
GEARY, CG .
JOURNAL OF CLINICAL PATHOLOGY, 1982, 35 (06) :617-619
[10]  
SILVAIN C, 1989, GASTROEN CLIN BIOL, V13, P834
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