MEMBRANOUS LIPODYSTROPHY - MR IMAGING APPEARANCE OF THE BRAIN

被引：18
作者：
ARAKI, T
OHBA, H
MONZAWA, S
SAKUYAMA, K
HACHIYA, J
SEKI, T
TAKAHASHI, Y
YAMAGUCHI, M
机构：
[1] KYORIN UNIV, DEPT RADIOL, MITAKA, TOKYO 181, JAPAN
[2] ST MARIANNA MED UNIV, YOKOHAMA SEIBU HOSP, DEPT RADIOL, YOKOHAMA, KANAGAWA, JAPAN
[3] ST MARIANNA MED UNIV, YOKOHAMA SEIBU HOSP, DEPT INTERNAL MED 3, YOKOHAMA, KANAGAWA, JAPAN
来源：
RADIOLOGY | 1991年 / 180卷 / 03期
关键词：
BONES; OSTEOCHONDRODYSPLASIAS; BRAIN; ATROPHY; MR STUDIES; WHITE MATTER; DEMENTIA;
D O I：
10.1148/radiology.180.3.1871295
中图分类号：
R8 [特种医学]; R445 [影像诊断学];
学科分类号：
1002 ; 100207 ; 1009 ;
摘要：
Five patients with membranous lipodystrophy (lipomembranous polycystic osteodysplasia with progressive dementia) underwent magnetic resonance (MR) imaging of the brain. T2-weighted MR images showed atrophied cerebral white matter with dilated ventricles; increased signal intensity of the white matter; and decreased signal intensity of the thalamus, putamen, caudate nucleus, and cerebral cortex. Although each single finding is not specific, the combination of the above MR findings when coupled with skeletal lesions strongly suggests this rare disease.
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页码：793 / 797
页数：5
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