Enlarged Vestibular Aqueduct Syndrome. Report on Four Cases

被引:0
作者
Taha, Muhamad [1 ]
Plaza, Guillermo [1 ]
Montojo, Jose [1 ]
Urbasos, Maria [2 ]
Hernando, Ana [2 ]
机构
[1] Hosp Fuenlabrada, Serv Otorinolaringol, Camino Molino 2, Madrid 28942, Spain
[2] Hosp Fuenlabrada, Serv Radiodiagnost, Madrid, Spain
来源
ACTA OTORRINOLARINGOLOGICA ESPANOLA | 2008年 / 59卷 / 10期
关键词
Enlarged vestibular aqueduct syndrome; Sensorineural hearing loss; Computed tomography; Magnetic resonance imaging;
D O I
暂无
中图分类号
R76 [耳鼻咽喉科学];
学科分类号
100213 ;
摘要
Although enlarged vestibular aqueduct syndrome (EVAS) has been reported to be one of the most common anomalies associated with sensorineural hearing loss, the mechanism of such loss is unclear, and there are no established criteria for diagnosis. We report 4 patients with sensorineural hearing loss that were diagnosed during the last year in our department of EVAS. We review the diagnostic criteria of this syndrome.
引用
收藏
页码:506 / 508
页数:3
相关论文
共 30 条
  • [11] Enlarged vestibular aqueduct:: looking for genotypic-phenotypic correlations
    Gonzalez-Garcia, Jose Angel
    Ibanez, Andres
    Ramirez-Camacho, Rafael
    Rodriguez, Antonio
    Garcia-Berrocal, Jose Ramon
    Trinidad, Almudena
    [J]. EUROPEAN ARCHIVES OF OTO-RHINO-LARYNGOLOGY, 2006, 263 (11) : 971 - 976
  • [12] Familial large vestibular aqueduct syndrome
    Griffith, AJ
    Arts, HA
    Downs, C
    Innis, JW
    Shepard, NT
    Sheldon, S
    Gebarski, SS
    [J]. LARYNGOSCOPE, 1996, 106 (08) : 960 - 965
  • [13] THE ENDOLYMPHATIC SAC IN THE MONDINI DISORDER
    GUSSEN, R
    [J]. ARCHIVES OF OTO-RHINO-LARYNGOLOGY-ARCHIV FUR OHREN-NASEN-UND KEHLKOPFHEILKUNDE, 1985, 242 (01): : 71 - 76
  • [14] Ieda Maria I, 2006, OTOL NEUROTOL, V27, P788
  • [15] JACKLER RK, 1989, LARYNGOSCOPE, V99, P1238
  • [16] KODAMA A, 1982, ANN OTO RHINOL LARYN, V91, P13
  • [17] KODAMA A, 1982, ANN OTO RHINOL LARYN, V91, P3
  • [18] LEVENSON MJ, 1989, ARCH OTOLARYNGOL, V115, P54
  • [19] Vestibular abnormalities in charge association
    Murofushi, T
    Ouvrier, RA
    Parker, GD
    Graham, RI
    daSilva, M
    Halmagyi, GM
    [J]. ANNALS OF OTOLOGY RHINOLOGY AND LARYNGOLOGY, 1997, 106 (02) : 129 - 134
  • [20] Vertigo and the enlarged vestibular aqueduct syndrome
    Oh, AK
    Ishiyama, A
    Baloh, RW
    [J]. JOURNAL OF NEUROLOGY, 2001, 248 (11) : 971 - 974