Arrhythmogenic right ventricular cardiomyopathy/dysplasia is a clinically difficult to define entity despite invasive and complex diagnostic approach (CT, NMR imaging). The value of ECG and echocardiography as screening methods by evaluation of subtle findings such as T wave inversions in right precordial leads and localised dilatations of different parts of the right ventricle shall be demonstrated by two case reports with clear autoptic and bioptic diagnosis of the disease. A recollection of simple diagnostic methods in order to make a decision on using invasive and complex diagnostic approach in right ventricular arrhythmia seems necessary.