DELAYED DIAGNOSIS OF CONGENITAL ADRENAL-GLAND HYPERPLASIA DUE TO 11-BETA-HYDROXYLASE DEFICIENCY

被引：0
作者：
FOURCADE, L
VANDEWALLE, JP
DENORAY, G
MAFART, B
GRAS, C
TOUZE, JE
机构：
来源：
SEMAINE DES HOPITAUX | 1995年 / 71卷 / 3-4期
关键词：
ADRENAL HYPERPLASIA; CONGENITAL; HYPERTENSION; HYPOKALEMIA; TOMOGRAPHY; X-RAY COMPUTED;
D O I：
暂无
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
11-beta-hydroxylase deficiency is an abnormality of the synthesis of adrenal gland steroids that is usually diagnosed during infancy or childhood. A case diagnosed in a 55-year-old male with severe arterial hypertension and hypokalemia is reported. Hormone assays and computed tomography findings established the diagnosis. Imaging studies showed extensive atheroma lesions. A brief review of the literature was conducted to examine the features of this condition, which is rarely recognized in adulthood.
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页码：98 / 101
页数：4
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