ENHANCED DEGRADATION OF TRYPSIN-TREATED LOW-DENSITY LIPOPROTEIN BY FIBROBLASTS FROM A PATIENT WITH HOMOZYGOUS FAMILIAL HYPERCHOLESTEROLEMIA

被引:21
作者
CAREW, TE [1 ]
CHAPMAN, MJ [1 ]
GOLDSTEIN, S [1 ]
STEINBERG, D [1 ]
机构
[1] INST NATL SANTE & RECH MED,UNITE RECH METAB LIPIDES,UNITE 35,F-94010 CRETEIL,FRANCE
关键词
D O I
10.1016/0005-2760(78)90115-7
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:171 / 175
页数:5
相关论文
共 12 条
[1]   ANALYSIS OF A MUTANT STRAIN OF HUMAN FIBROBLASTS WITH A DEFECT IN INTERNALIZATION OF RECEPTOR-BOUND LOW-DENSITY LIPOPROTEIN [J].
BROWN, MS ;
GOLDSTEIN, JL .
CELL, 1976, 9 (04) :663-674
[2]   RECEPTOR-MEDIATED CONTROL OF CHOLESTEROL-METABOLISM [J].
BROWN, MS ;
GOLDSTEIN, JL .
SCIENCE, 1976, 191 (4223) :150-154
[3]   REGULATION OF ACTIVITY OF LOW-DENSITY LIPOPROTEIN RECEPTOR IN HUMAN FIBROBLASTS [J].
BROWN, MS ;
GOLDSTEIN, JL .
CELL, 1975, 6 (03) :307-316
[4]  
CHAPMAN MJ, 1976, ATHEROSCLEROSIS, V25, P267
[5]  
CHAPMAN MJ, 1976, 19TH P INT C BIOCH L, P12
[6]   ALTERATIONS IN CELL-SURFACE GLYCOSPHINGOLIPIDS AND OTHER LIPID CLASSES OF FIBROBLASTS IN FAMILIAL HYPERCHOLESTEROLEMIA [J].
CHATTERJEE, S ;
SEKERKE, CS ;
KWITEROVICH, PO .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1976, 73 (12) :4339-4343
[7]   PLAQUE PRODUCTION BY THE POLYOMA VIRUS [J].
DULBECCO, R ;
FREEMAN, G .
VIROLOGY, 1959, 8 (03) :396-397
[8]  
FOGELMAN AM, 1977, J BIOL CHEM, V252, P644
[9]   INTERACTION BETWEEN HIGH-DENSITY AND LOW-DENSITY LIPOPROTEINS DURING UPTAKE AND DEGRADATION BY CULTURED HUMAN FIBROBLASTS [J].
MILLER, NE ;
WEINSTEIN, DB ;
CAREW, TE ;
KOSCHINSKY, T ;
STEINBERG, D .
JOURNAL OF CLINICAL INVESTIGATION, 1977, 60 (01) :78-88
[10]  
MILLER NE, J LIPID RES