PULMONARY ALVEOLAR MICROLITHIASIS - REVIEW OF TURKISH REPORTS

被引:60
作者
UCAN, ES
KEYF, AI
AYDILEK, R
YALCIN, Z
SEBIT, S
KUDU, M
OK, U
机构
[1] HAVDARPASA TRAINING HOSP,GULHANE MIL MED FAC,IZMIR,TURKEY
[2] DOKUZ EYLUL UNIV,SCH MED,DEPT CHEST DIS,IZMIR,TURKEY
关键词
D O I
10.1136/thx.48.2.171
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
Pulmonary alveolar microlithiasis is a rare disorder, only 173 cases having been reported worldwide. Fifty two cases from Turkey are reported, 49 of which have previously been described only in Turkish publications. The mean age of the patients was 27 (SD 12) years, 34 were male, and 10 were symptomless. In 40 of the 52 cases diagnosis was confirmed histopathologically. Nineteen cases were diagnosed in siblings. This high rate suggests that pulmonary alveolar microlithiasis is a familial disease, which, though rare, is for unknown reasons most common in Turkey.
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页码:171 / 173
页数:3
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