REGIONAL MACRODONTIA AND REGIONAL BONY ENLARGEMENT ASSOCIATED WITH CONGENITAL INFILTRATING LIPOMATOSIS OF THE FACE PRESENTING AS UNILATERAL FACIAL HYPERPLASIA - BRIEF REVIEW AND CASE-REPORT

Congenital infiltrating lipomatosis of the face (CIL-F) is a rare lesion. Presented here is a review of the literature concerning this condition, with the report of a case with clinical signs indistinguishable from those of unilateral facial hyperplasia. Previously unreported clinical and radiographic features of regional bony hypertrophy and macrodontia associated with this case of CIL-F are described and the propostition raised that previously reported cases of unilateral facial hyperplasia may have been due to CIL-F. It is suggested that the clinical findings in this case of facial asymmetry associated with CIL-F, regional macrodontia and regional bony enlargement may constitute a previously undescribed syndrome. © 1990 Munksgaard International Publishers Ltd.