Lung agenesis is a rare condition which prognosis widely depends on associated malformations. Clinical presentation is so variable and diagnosis is often made in childhood. Here, we present a case of a 20-year-old girl who was admitted because of a spontaneous pneumothorax. Explorations concluded at a left lung agenesis, a hyperinflated right lung crossing the midline with a corresponding pneumothorax. There was no malformation else. This congenital condition and treatment for this rare presentation are discussed in detail.
机构:
Univ Nove Julho, Dept Med, Sao Paulo, SP, BrazilUniv Nove Julho, Dept Med, Sao Paulo, SP, Brazil
Silveira, Joao V.
Junqueira, Flavia P.
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机构:
DASA SP, Delboni Auriemo, Dept Radiol, Sao Paulo, SP, BrazilUniv Nove Julho, Dept Med, Sao Paulo, SP, Brazil
Junqueira, Flavia P.
Silveira, Cylmara G.
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机构:
Univ Nove Julho, Dept Pediat, Sao Paulo, SP, BrazilUniv Nove Julho, Dept Med, Sao Paulo, SP, Brazil
Silveira, Cylmara G.
Consolim-Colombo, Fernanda M.
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机构:
Univ Nove Julho, Dept Catdiol, Sao Paulo, SP, Brazil
Univ Sao Paulo Brazil InCor 3, Dept Cardiol, Inst Coracao, Sao Paulo, SP, BrazilUniv Nove Julho, Dept Med, Sao Paulo, SP, Brazil
Consolim-Colombo, Fernanda M.
AMERICAN JOURNAL OF CASE REPORTS,
2019,
20
: 228
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232