SCLEROSING CHOLANGITIS ASSOCIATED WITH MULTIFOCAL FIBROSIS - A CASE-REPORT

被引:44
作者
LAITT, RD
HUBSCHER, SG
BUCKELS, JA
DARBY, S
ELIAS, E
机构
[1] QUEEN ELIZABETH MED CTR,LIVER UNIT,BIRMINGHAM B15 2TH,W MIDLANDS,ENGLAND
[2] QUEEN ELIZABETH MED CTR,DEPT PATHOL,BIRMINGHAM B15 2TH,W MIDLANDS,ENGLAND
[3] QUEEN ELIZABETH MED CTR,DEPT RADIOL,BIRMINGHAM B15 2TH,W MIDLANDS,ENGLAND
关键词
D O I
10.1136/gut.33.10.1430
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
The association of sclerosing cholangitis, retroperitoneal fibrosis, and Riedel's thyroiditis has been reported twice before,1 2 and on both occasions the authors successfully used steroids to control the fibrotic process. A further case of fibrosis with this triad of organ involvement in which a combination of surgery and steroid treatment has arrested disease progression is described. This suggests an inappropriate immune response in this type of fibrotic overlap syndrome.
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页码:1430 / 1432
页数:3
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