HUMAN ERYTHROCYTE PHOSPHORIBOSYLPYROPHOSPHATE SYNTHETASE MUTATIONALLY ALTERED IN REGULATORY PROPERTIES

被引:76
作者
SPERLING, O
PERSKYBR.S
BOER, P
DEVRIES, A
机构
[1] TEL AVIV UNIV,BEILINSON HOSP,MED SCH,ROGOFF WELLCOME MED RES INST,PETAH TIKUA,ISRAEL
[2] TEL AVIV UNIV,BEILINSON HOSP,MED SCH,DEPT MED,METAB UNIT,PETAH TIKVA,ISRAEL
来源
BIOCHEMICAL MEDICINE | 1973年 / 7卷 / 03期
关键词
D O I
10.1016/0006-2944(73)90059-8
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:389 / 395
页数:7
相关论文
共 20 条
[1]  
AMES BN, 1963, SYNTHESIS STRUCTURE, V28, P349
[2]  
BARLETT GR, 1959, J BIOL CHEM, V234, P449
[3]   PHOSPHORIBOSYLPYROPHOSPHATE IN MAN - BIOCHEMICAL AND CLINICAL SIGNIFICANCE [J].
FOX, IH ;
KELLEY, WN .
ANNALS OF INTERNAL MEDICINE, 1971, 74 (03) :424-+
[4]  
GOLDTHWAIT DA, 1956, J BIOL CHEM, V222, P1051
[5]   VARIATIONS IN PURINE METABOLISM OF CULTURED SKIN FIBROBLASTS FROM PATIENTS WITH GOUT [J].
HENDERSON, JF ;
ROSENBLOOM, FM ;
KELLEY, WN ;
SEEGMILLER, JE .
JOURNAL OF CLINICAL INVESTIGATION, 1968, 47 (07) :1511-+
[6]  
HENDERSON JF, 1967, CANCER RES, V27, P1773
[7]  
HERSHKO A, 1968, ISRAEL J MED SCI, V4, P939
[8]   REGULATION OF SYNTHESIS OF 5-PHOSPHORIBOSYL-I-PYROPHOSPHATE IN INTACT RED BLOOD CELLS AND IN CELL-FREE PREPARATIONS [J].
HERSHKO, A ;
RAZIN, A ;
MAGER, J .
BIOCHIMICA ET BIOPHYSICA ACTA, 1969, 184 (01) :64-&
[9]   ACCELERATED TURNOVER OF PHOSPHORIBOSYLPYROPHOSPHATE, A PURINE NUCLEOTIDE PRECURSOR, IN CERTAIN GOUTY SUBJECTS [J].
JONES, OW ;
ASHTON, DM ;
WYNGAARDEN, JB .
JOURNAL OF CLINICAL INVESTIGATION, 1962, 41 (09) :1805-&
[10]   REGULATION OF PURINE BIOSYNTHESIS IN CULTURED HUMAN CELLS .1. EFFECTS OF OROTIC ACID [J].
KELLEY, WN ;
FOX, IH ;
WYNGAARDEN, JB .
BIOCHIMICA ET BIOPHYSICA ACTA, 1970, 215 (03) :512-+