SOLITARY FIBROUS TUMOR OF THE ORBIT

被引:198
作者
DORFMAN, DM
TO, K
DICKERSIN, GR
ROSENBERG, AE
PILCH, BZ
机构
[1] HARVARD UNIV, SCH MED, DEPT PATHOL, BOSTON, MA 02115 USA
[2] MASSACHUSETTS GEN HOSP, DEPT PATHOL, BOSTON, MA 02114 USA
[3] MASSACHUSETTS EYE & EAR INFIRM, DEPT PATHOL, BOSTON, MA 02114 USA
[4] BROWN UNIV, RHODE ISL HOSP, SCH MED, DEPT OPHTHALMOL & PATHOL, PROVIDENCE, RI 02903 USA
[5] PROVIDENCE VET ADM MED CTR, DEPT OPHTHALMOL & PATHOL, PROVIDENCE, RI USA
关键词
SOLITARY FIBROUS TUMOR; LOCALIZED FIBROUS MESOTHELIOMA; ORBIT;
D O I
10.1097/00000478-199403000-00008
中图分类号
R36 [病理学];
学科分类号
100104 ;
摘要
We report three cases of an orbital soft tissue lesion that fulfills the histologic, immunohistochemical, and electron microscopic criteria for solitary fibrous tumor, an entity previously described as a pleural tumor, but recently reported to occur in other locations. All three patients presented with proptosis. Two of the patients were cured by simple excision, and one patient had two recurrences, the last recurrence incompletely excised. The findings indicate that solitary fibrous tumor can occur in the orbit and, like solitary fibrous tumors of other anatomic sites, may behave in a nonaggressive or occasionally, locally aggressive fashion, with as yet no metastatic potential demonstrated in orbital lesions.
引用
收藏
页码:281 / 287
页数:7
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