Orthodontic treatment of a patient with recessive dystrophic epidermolysis bullosa: a case report

被引:11
作者
Pacheco, Wellington [1 ]
de Sousa Araugio, Rafael [1 ]
机构
[1] Pontific Catholic Univ Minas Gerais PUC Minas, Belo Horizonte, MG, Brazil
关键词
epidermolysis bullosa; genetic disorder; orthodontic treatment; trismus;
D O I
10.1111/j.1754-4505.2008.00028.x
中图分类号
R78 [口腔科学];
学科分类号
1003 ;
摘要
Epidermolysis bullosa (EB) represents a heterogeneous group of hereditary, chronic, non-inflammatory skin pathologies. Recessive dystrophic epidermolysis bullosa (RDEB) is characterized by sub-lamina dura separation, due to blistering below the lamina densa of the basement membrane zone, and is associated with the absence of Type VII collagen fibers. The mouth, pharyngeal, and esophageal mucosa are compromised by scarring and tissue contraction. The purpose of this article was to present a case report on an orthodontic patient with RDEB.
引用
收藏
页码:136 / 139
页数:4
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