PERIODONTITIS ASSOCIATED WITH PAPILLON-LEFEVRE SYNDROME

被引:41
作者
BIMSTEIN, E
LUSTMANN, J
SELA, MN
BENNERIAH, Z
SOSKOLNE, WA
机构
[1] HEBREW UNIV JERUSALEM,HADASSAH FAC DENT MED,DEPT ORAL & MAXILLOFACIAL SURG,JERUSALEM,ISRAEL
[2] HEBREW UNIV JERUSALEM,HADDASSAH FAC DENT MED,DEPT ORAL BIOL,JERUSALEM,ISRAEL
[3] HEBREW UNIV JERUSALEM,HADDASSAH FAC DENT MED,DEPT HUMAN GENET,JERUSALEM,ISRAEL
[4] HEBREW UNIV JERUSALEM,HADDASSAH FAC DENT MED,DEPT PERIODONT,JERUSALEM,ISRAEL
关键词
D O I
10.1902/jop.1990.61.6.373
中图分类号
R78 [口腔科学];
学科分类号
1003 ;
摘要
The predominant subgingival microflora, host immune response, and genetic history of a 14-year-old girl with Papillon-Lefèvre Syndrome (PLS) are reported. The patient had high counts of Actinobacillus actinomycetemcomitans and surface translocating bacteria. She had significantly raised levels of antibodies to five of the bacterial species studied with the levels to A. actinomycetemcomitans remaining high after antibiotic therapy. The polymorphonuclear leukocytes (PMN) also released significantly increased amounts of O2 compared to controls. The data presented support a role for A. actinomycetemcomitans and PMN dysfunction in the pathogenesis of PLS.
引用
收藏
页码:373 / 377
页数:5
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