KI-1-POSITIVE LARGE-CELL CUTANEOUS LYMPHOMA MIMICKING A STEWART-TREVES ANGIOSARCOMA

被引:14
|
作者
BEYLOTBARRY, M [1 ]
VERGIER, B [1 ]
BEYLOT, C [1 ]
DEMASCAREL, A [1 ]
DOUTRE, MS [1 ]
机构
[1] CHU BORDEAUX,HOP HAUT LEVEQUE,ANATOMOPATHOL LAB,F-33604 PESSAC,FRANCE
关键词
ANAPLASTIC LARGE-CELL LYMPHOMA; STEWART-TREVES SYNDROME; IMMUNOHISTOCHEMISTRY; CHRONIC LYMPHEDEMA;
D O I
10.1159/000246641
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Anaplastic large-cell cutaneous lymphomas (ALCL) represent a heterogeneous group. Primitive cutaneous lymphomas are exceptional, sometimes with a deceptive clinical aspect, but must be considered as a distinct clinicopathologic entity, We report a case of a cutaneous ALCL, appearing 7 years after a homolateral Hodgkin ganglionic lymphoma and occurring on a chronic lymphoedema of the arm. A Stewart-Treves angiosarcoma was suggested owing to its location, vascular aspect and low histologic differentiation. Immunohistochemistry was helpful in making the diagnosis of ALCL. Southern blotting analysis revealed a rearrangement of the beta-chain of the T-receptor gene, thus suggesting the T-cell origin of this lymphoma.
引用
收藏
页码:77 / 82
页数:6
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