VARIANT VONWILLEBRANDS DISEASE - CHARACTERIZATION OF 2 SUBTYPES BY ANALYSIS OF MULTIMERIC COMPOSITION OF FACTOR 8 VONWILLEBRAND-FACTOR IN PLASMA AND PLATELETS

被引:547
作者
RUGGERI, ZM
ZIMMERMAN, TS
机构
关键词
D O I
10.1172/JCI109795
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
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页码:1318 / 1325
页数:8
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共 27 条
[1]  
BARBER AJ, 1970, J BIOL CHEM, V245, P6357
[2]   DISULFIDE BONDS AND QUATERNARY STRUCTURE OF FACTOR-VIII-VONWILLEBRAND FACTOR [J].
COUNTS, RB ;
PASKELL, SL ;
ELGEE, SK .
JOURNAL OF CLINICAL INVESTIGATION, 1978, 62 (03) :702-709
[3]  
DUNKER AK, 1976, BIOCHEM J, V153, P191, DOI 10.1042/bj1530191
[4]  
FASS DN, 1978, J LAB CLIN MED, V91, P307
[5]   VONWILLEBRANDS DISEASE - COMBINED QUALITATIVE AND QUANTITATIVE ABNORMALITIES [J].
GRALNICK, HR ;
SULTAN, Y ;
COLLER, BS .
NEW ENGLAND JOURNAL OF MEDICINE, 1977, 296 (18) :1024-1030
[6]   VARIANT OF FACTOR-VIII RELATED ANTIGEN [J].
KERNOFF, PBA ;
GRUSON, R ;
RIZZA, CR .
BRITISH JOURNAL OF HAEMATOLOGY, 1974, 26 (03) :435-+
[7]   ACTIVE RELEASE OF HUMAN PLATELET FACTOR-VIII-RELATED ANTIGEN BY ADENOSINE-DIPHOSPHATE, COLLAGEN, AND THROMBIN [J].
KOUTTS, J ;
WALSH, PN ;
PLOW, EF ;
FENTON, JW ;
BOUMA, BN ;
ZIMMERMAN, TS .
JOURNAL OF CLINICAL INVESTIGATION, 1978, 62 (06) :1255-1263
[8]   IMMUNOGLOBULINS CYTOPHILIC FOR HUMAN LYMPHOCYTES, MONOCYTES, AND NEUTROPHILS [J].
LAWRENCE, DA ;
WEIGLE, WO ;
SPIEGELBERG, HL .
JOURNAL OF CLINICAL INVESTIGATION, 1975, 55 (02) :368-376
[9]  
LEGAZ MG, 1973, J BIOLOGICAL CHEM, V218, P3946
[10]   A METHOD OF TRACE IODINATION OF PROTEINS FOR IMMUNOLOGIC STUDIES [J].
MCCONAHEY, PJ ;
DIXON, FJ .
INTERNATIONAL ARCHIVES OF ALLERGY AND APPLIED IMMUNOLOGY, 1966, 29 (02) :185-+