PLASMA-EXCHANGE FOR REFSUMS DISEASE

被引:13
作者
GIBBERD, FB
机构
[1] Department of Neurology, Westminster Hospital, London
来源
TRANSFUSION SCIENCE | 1993年 / 14卷 / 01期
关键词
D O I
10.1016/0955-3886(93)90049-Z
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Five patients with Refsum's disease were treated by plasma exchange. Lowering the plasma phytanic acid by plasma exchange in patients acutely ill with Refsum's disease produced clinical improvement. Plasma exchange is indicated in Refsum's disease when there is a worsening clinical condition. Occasionally, failure of dietary control of Refsum's disease may necessitate plasma exchange.
引用
收藏
页码:23 / 26
页数:4
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