Data on cytochrome c oxidase assembly in mice and human fibroblasts or tissues induced by SURF1 defect

被引：1
|
作者：
Kovarova, Nikola [1 ]
Pecina, Petr [1 ]
Nuskova, Hana [1 ]
Vrbacky, Marek [1 ]
Zeviani, Massimo [2 ,3 ]
Mracek, Tomas [1 ]
Viscomi, Carlo [3 ]
Houstek, Josef [1 ]
机构：
[1] Czech Acad Sci, Inst Physiol, Videnska 1083, Prague, Czech Republic
[2] Inst Neurol C Besta, Mol Neurogenet Unit, Via Temolo 4, I-20126 Milan, Italy
[3] MRC Mitochondrial Biol Unit, Wellcome Trust MRC Bldg, Cambridge CB2 0XY, England
来源：
DATA IN BRIEF | 2016年 / 7卷
基金：
英国医学研究理事会;
关键词：
Cytochrome c oxidase; Respiratory chain; SURF1; Knockout; Doxycycline;
D O I：
10.1016/j.dib.2016.03.065
中图分类号：
O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];
学科分类号：
07 ; 0710 ; 09 ;
摘要：
This paper describes data related to a research article entitled "Tissue- and species-specific differences in cytochrome c oxidase assembly induced by SURF] defects" [1] This paper includes data of the quantitative analysis of individual forms of respiratory chain complexes I, III and IV present in SURF] knockout (SURF]-I-) and control (SURF1(+/+)) mouse fibroblasts and tissues and in fibroblasts of human control and patients with SURF] gene mutation. Also it includes data demonstrating response of complex IV, cytochrome c oxidase (COX), to reversible inhibition of mitochondria[ translation in SURF1(-'-) mouse and SURF1 patient fibroblast cell lines. (C) 2016 The Authors. Published by Elsevier Inc.
引用
收藏
页码：1004 / 1009
页数：6
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