Data on cytochrome c oxidase assembly in mice and human fibroblasts or tissues induced by SURF1 defect

被引：1

作者：

Kovarova, Nikola ^{[1
]}

Pecina, Petr ^{[1
]}

Nuskova, Hana ^{[1
]}

Vrbacky, Marek ^{[1
]}

Zeviani, Massimo ^{[2
,3
]}

Mracek, Tomas ^{[1
]}

Viscomi, Carlo ^{[3
]}

Houstek, Josef ^{[1
]}

机构：

[1] Czech Acad Sci, Inst Physiol, Videnska 1083, Prague, Czech Republic

[2] Inst Neurol C Besta, Mol Neurogenet Unit, Via Temolo 4, I-20126 Milan, Italy

[3] MRC Mitochondrial Biol Unit, Wellcome Trust MRC Bldg, Cambridge CB2 0XY, England

来源：

DATA IN BRIEF | 2016年 / 7卷

基金：

英国医学研究理事会;

关键词：

Cytochrome c oxidase; Respiratory chain; SURF1; Knockout; Doxycycline;

D O I：

10.1016/j.dib.2016.03.065

中图分类号：

O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];

学科分类号：

07 ; 0710 ; 09 ;

摘要：

This paper describes data related to a research article entitled "Tissue- and species-specific differences in cytochrome c oxidase assembly induced by SURF] defects" [1] This paper includes data of the quantitative analysis of individual forms of respiratory chain complexes I, III and IV present in SURF] knockout (SURF]-I-) and control (SURF1(+/+)) mouse fibroblasts and tissues and in fibroblasts of human control and patients with SURF] gene mutation. Also it includes data demonstrating response of complex IV, cytochrome c oxidase (COX), to reversible inhibition of mitochondria[ translation in SURF1(-'-) mouse and SURF1 patient fibroblast cell lines. (C) 2016 The Authors. Published by Elsevier Inc.

引用

页码：1004 / 1009

页数：6

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