SERIAL MRI IN FUKUYAMA TYPE CONGENITAL MUSCULAR-DYSTROPHY

被引:11
作者
AIHARA, M [1 ]
TANABE, Y [1 ]
KATO, K [1 ]
机构
[1] CHIBA CHILDRENS HOSP,DEPT NEUROL,CHIBA,JAPAN
关键词
FUKUYAMA TYPE CONGENITAL MUSCULAR DYSTROPHY; CENTRAL NERVOUS SYSTEM; DELAYED MYELINATION; MAGNETIC RESONANCE IMAGING;
D O I
10.1007/BF00596498
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Serial MRI of the brain of a female infant with Fukuyama type congenital muscular dystrophy (FCMD) is presented. Initial MRI revealed diffuse abnormal signal in the cerebral white matter extending peripherally On follow-up studies, the abnormal signals disappeared or decreased from the posterior to anterior, and from central to peripheral. These changes in signal intensity correlate well with the process of myelination as demonstrated in histochemical studies. It appears that the abnormal signals in FCMD are caused by delayed myelination. When abnormal signal intensity is seen in the cerebral white matter of a developmentally delayed infant, serial MRI may be used to follow the course of the illness.
引用
收藏
页码:396 / 398
页数:3
相关论文
共 20 条
[1]  
AIHARA M, 1986, PROG COMPUT TOMOGR T, V8, P537
[2]   NORMAL MATURATION OF THE NEONATAL AND INFANT BRAIN - MR IMAGING AT 1.5 T [J].
BARKOVICH, AJ ;
KJOS, BO ;
JACKSON, DE ;
NORMAN, D .
RADIOLOGY, 1988, 166 (01) :173-180
[3]   SEQUENCE OF CENTRAL-NERVOUS-SYSTEM MYELINATION IN HUMAN INFANCY .1. AN AUTOPSY STUDY OF MYELINATION [J].
BRODY, BA ;
KINNEY, HC ;
KLOMAN, AS ;
GILLES, FH .
JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY, 1987, 46 (03) :283-301
[4]   MAPPING OF NORMAL BRAIN MATURATION IN INFANTS ON PHASE-SENSITIVE INVERSION RECOVERY MR IMAGES [J].
CHRISTOPHE, C ;
MULLER, MF ;
BALERIAUX, D ;
KAHN, A ;
PARDOU, A ;
PERLMUTTER, N ;
SZLIWOWSKI, H ;
SEGEBARTH, C .
NEURORADIOLOGY, 1990, 32 (03) :173-178
[5]   MR EVALUATION OF EARLY MYELINATION PATTERNS IN NORMAL AND DEVELOPMENTALLY DELAYED INFANTS [J].
DIETRICH, RB ;
BRADLEY, WG ;
ZARAGOZA, EJ ;
OTTO, RJ ;
TAIRA, RK ;
WILSON, GH ;
KANGARLOO, H .
AMERICAN JOURNAL OF ROENTGENOLOGY, 1988, 150 (04) :889-896
[6]   CONGENITAL MUSCULAR-DYSTROPHY AND CEREBRAL CT-SCAN ANOMALIES - RESULTS OF A COLLABORATIVE STUDY OF THE SOCIETE-DE-NEUROLOGIE-INFANTILE [J].
ECHENNE, B ;
ARTHUIS, M ;
BILLARD, C ;
CAMPOSCASTELLO, J ;
CASTEL, Y ;
DULAC, O ;
FONTAN, D ;
GAUTHIER, A ;
KULAKOWSKI, S ;
DEMEURON, G ;
MOORE, JR ;
NIETOBARRERA, M ;
PAGES, M ;
PARAIN, D ;
PAVONE, L ;
PONSOT, G .
JOURNAL OF THE NEUROLOGICAL SCIENCES, 1986, 75 (01) :7-22
[7]  
Engel AG, 1986, MYOLOGY, V2, P1367
[8]  
FUKUYAMA Y, 1981, BRAIN DEV-JPN, V3, P1
[9]  
HOLLAND BA, 1986, AM J NEURORADIOL, V7, P201
[10]   FUKUYAMA-TYPE CONGENITAL MUSCULAR-DYSTROPHY [J].
ISHIKAWA, A .
ARCHIVES OF NEUROLOGY, 1982, 39 (10) :671-671