Adenocarcinoma of the endolymphatic sac in von Hippel-Lindau disease. A case report

被引：0

作者：

Martinez-Miravete, P. ^{[1
]}

Dominguez, P. ^{[1
]}

Zubieta, J. L. ^{[1
]}

Manrique, M. ^{[2
]}

机构：

[1] Univ Navarra, Serv Radiol, Pamplona, Spain

[2] Univ Navarra, Fac Med, Clin Univ, Serv Otorrinolaringol, Pamplona, Spain

来源：

RADIOLOGIA | 2007年 / 49卷 / 04期

关键词：

von Hippel-Lindau disease; endolymphatic sac; adenocarcinoma;

D O I：

10.1016/S0033-8338(07)73773-6

中图分类号：

R8 [特种医学]; R445 [影像诊断学];

学科分类号：

1002 ; 100207 ; 1009 ;

摘要：

Tumors originating in the endolymphatic system are extremely rare, and very few articles have been published about this type of tumors. Up to 15% of cases are associated to von Hippel-Lindau disease. This article describes the case of a patient previously diagnosed with von Hippel-Landau disease that presented a sudden loss of hearing in the left ear. Specific imaging tests (computed tomography [CT] and magnetic resonance imaging [MRI]) showed the presence of a neoplasm originating in the left endolymphatic sac. Histological analysis of the surgical specimen determined it corresponded to an adenocarcinoma of the endolymphatic sac.

引用

页码：287 / 289

页数：3

共 15 条

[1] COMPUTER-AIDED AND GRAPHIC RECONSTRUCTION OF THE HUMAN ENDOLYMPHATIC DUCT AND SAC - A METHOD FOR COMPARING MENIERES AND NON-MENIERES DISEASE CASES [J].