CHRONIC RELAPSING NEUROPATHY ASSOCIATED WITH CASTLEMANS DISEASE (ANGIOFOLLICULAR LYMPH-NODE HYPERPLASIA)

被引:10
作者
VINGERHOETS, F
KUNTZER, T
DELACRETAZ, F
STECK, AJ
KNECHT, H
BOGOUSSLAVSKY, J
MEIER, C
REGLI, F
机构
[1] CHU VAUDOIS,SERV NEUROL,CH-1011 LAUSANNE,SWITZERLAND
[2] CHU VAUDOIS,INST UNIV PATHOL,CH-1011 LAUSANNE,SWITZERLAND
[3] CHU VAUDOIS,DIV HEMATOL,CH-1011 LAUSANNE,SWITZERLAND
[4] INSELSPITAL BERN,MORPHOL FORSCH LAB,CH-3010 BERN,SWITZERLAND
关键词
DEMYELINATING NEUROPATHY; EPSTEIN-BARR VIRUS; ANGIOFOLLICULAR LYMPH NODE HYPERPLASIA; CASTLEMANS DISEASE;
D O I
10.1159/000117156
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
We report a 17-year-old patient who presented a chronic relapsing sensorimotor demyelinating neuropathy with 6 relapses over a 7-year period, preceding by 4 years the diagnosis of a multicentric angiofollicular lymph node hyperplasia. A role for Epstein-Barr virus (EBV) as a trigger of the neuropathy may be suggested by the presence of EBV DNA in the biopsied abdominal adenopathies. This unusual reported association seems to have a better prognosis than the known chronic progressive form of neuropathy associated with Castleman's disease and the Crow-Fukase syndrome.
引用
收藏
页码:336 / 340
页数:5
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