A Case of Hereditary Palmoplantar Keratoderma Associated with Primary Digital Clubbing

Palmoplantar keratodermas, also known as palmoplantar hyperkeratosis or keratosis palmaris et plantaris, are a group of diseases characterized by marked thickening of the skin of the palms and soles. Palmoplantar keratodermas may be acquired or hereditary. Clubbing is defined as hypertrophy of the soft tissue components of the digital pulp and increased longitudinal and horizontal curvature of the nail plate. Clubbing is usually acquired. The diagnosis of familial or idiopathic clubbing is made only after exclusion of underlying systemic diseases. Hereditary palmoplantar keratodermas may be associated with a wide variety of disorders. Herein we present a case of hereditary palmoplantar keratoderma in conjunction with primary digital clubbing, which is a rare association.