EVIDENCE FOR ENZYMIC DEFECT IN BETA-METHYLCROTONYLGLYCINURIA

被引:27
作者
GOMPERTZ, D [1 ]
GOODEY, PA [1 ]
BARTLETT, K [1 ]
机构
[1] ROY POSTGRAD MED SCH,DEPT MED,LONDON W12,ENGLAND
关键词
D O I
10.1016/0014-5793(73)80723-9
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:13 / 14
页数:2
相关论文
共 7 条
[1]   CARBOXYLATION OF BETA-METHYLCROTONYL COENZYME-A BY A PURIFIED ENZYME FROM CHICKEN LIVER [J].
DELCAMPILLOCAMPBELL, A ;
DEKKER, EE ;
COON, MJ .
BIOCHIMICA ET BIOPHYSICA ACTA, 1959, 31 (01) :290-292
[2]  
ELDJARN L, 1970, LANCET, V2, P521
[3]  
GOMPERTZ D, 1971, LANCET, V2, P22
[4]  
KNAPPE J, 1961, BIOCHEM Z, V335, P101
[5]  
LIPMANN F, 1945, J BIOL CHEM, V159, P21
[6]  
MELLMAN WJ, 1965, J LAB CLIN MED, V66, P980
[7]  
STADTMAN ER, 1957, METHODS ENZYMOLOGY, V3