NEW ABNORMAL HEMOGLOBIN (HB ABRUZZO, BETA-143 HIS -] ARG) WITH INCREASED OXYGEN-AFFINITY, IN 2 BROTHERS WITH HEMOLYTIC SYNDROME OF MEDITERRANEAN TYPE AND MARKED ERYTHROCYTOSIS

被引:0
|
作者
CHIARIONI, T
NARDI, E
PAPA, G
SASSO, GF
TENTORI, L
机构
[1] UNIV ROME, IST PATOL SPECIALE MED & METODOL CLIN, POLICLIN UMBERTO 1, I-00161 ROME, ITALY
[2] IST SUPER SANITA, VIALE REGINA ELENA 299, I-00161 ROME, ITALY
来源
NOUVELLE REVUE FRANCAISE D HEMATOLOGIE | 1974年 / 14卷 / 01期
关键词
D O I
暂无
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:67 / 79
页数:13
相关论文
共 30 条
  • [1] HEMOGLOBIN VANDERBILT (ALPHA-2-BETA-289SER-]ARG) - NEW HEMOGLOBIN WITH HIGH OXYGEN-AFFINITY AND COMPENSATORY ERYTHROCYTOSIS
    PANIKER, NV
    LIN, KTD
    KRANTZ, SB
    FLEXNER, JM
    WASSERMAN, BK
    PUETT, D
    BRITISH JOURNAL OF HAEMATOLOGY, 1978, 39 (02) : 249 - 258
  • [2] HEMOGLOBIN OHIO (BETA-142 ALA-]ASP) - A NEW ABNORMAL HEMOGLOBIN WITH HIGH OXYGEN-AFFINITY AND ERYTHROCYTOSIS
    MOOPENN, WF
    SCHNEIDER, RG
    SHIH, TB
    JONES, RT
    GOVINDARAJAN, S
    GOVINDARAJAN, PG
    PATCHEN, LC
    BLOOD, 1980, 56 (02) : 246 - 250
  • [3] HEMOGLOBIN ABRUZZO [BETA-143 (H21) HIS-]ARG] - CONSEQUENCES OF ALTERING 2,3-DIPHOSPHOGLYCERATE BINDING-SITE
    BONAVENTURA, C
    BONAVENTURA, J
    AMICONI, G
    TENTORI, L
    BRUNORI, M
    ANTONINI, E
    JOURNAL OF BIOLOGICAL CHEMISTRY, 1975, 250 (16) : 6273 - 6277
  • [4] HEMOGLOBIN SYRACUSE (BETA 143 HIS-]PRO), A NEW VARIANT WITH HIGHER OXYGEN-AFFINITY IN A FAMILY WITH POLYCYTHEMIA
    JENSEN, M
    KLINISCHE WOCHENSCHRIFT, 1974, 52 (23): : 1137 - 1137
  • [5] HB TROLLHATTAN [BETA-20(B2)VAL-]GLU] - HEMOGLOBIN-VARIANT WITH INCREASED OXYGEN-AFFINITY CAUSING ERYTHROCYTOSIS
    LANDIN, B
    BERGLUND, S
    LINDOFF, B
    EUROPEAN JOURNAL OF HAEMATOLOGY, 1994, 53 (01) : 21 - 25
  • [6] HB OKAZAKI [BETA-93(F8) CYS-]ARG], A NEW HEMOGLOBIN-VARIANT WITH INCREASED OXYGEN-AFFINITY AND INSTABILITY
    HARANO, K
    HARANO, T
    SHIBATA, S
    UEDA, S
    MORI, H
    SEKI, M
    FEBS LETTERS, 1984, 173 (01) : 45 - 47
  • [7] HEMOGLOBIN WOOD BETA-97(FG4) HIS -] LEU - NEW HIGH OXYGEN-AFFINITY HEMOGLOBIN ASSOCIATED WITH FAMILIAL ERYTHROCYTOSIS
    TAKETA, F
    HUANG, YP
    LIBNOCH, JA
    DESSEL, BH
    BIOCHIMICA ET BIOPHYSICA ACTA, 1975, 400 (02) : 348 - 353
  • [8] HEMOGLOBIN VANDERBILT (BETA-89, SER-]ARG) - NEW HEMOGLOBIN MUTANT WITH INCREASED OXYGEN-AFFINITY AND LOWERED RESPONSE TO 2,3-DIPHOSPHOGLYCERATE
    PUETT, D
    PANIKER, NV
    LIN, KD
    FLEXNER, JM
    WASSERMAN, BK
    KRANTZ, SB
    CLINICAL RESEARCH, 1977, 25 (01): : A53 - A53
  • [9] HEMOGLOBIN SYRACUSE (BETA143 HIS-]PRO) - NEW VARIANT WITH HIGH OXYGEN-AFFINITY DETECTED BY SPECIAL ELECTROPHORETIC METHODS
    JENSEN, M
    BUNN, HF
    NATHAN, DG
    OSKI, FA
    BLOOD, 1973, 42 (06) : 989 - 989
  • [10] HEMOGLOBIN LEGNANO (ALPHA-2 141 (HC3) ARG-]LEU BETA-2) - NEW ABNORMAL HUMAN HEMOGLOBIN WITH HIGH OXYGEN-AFFINITY
    MAVILIO, F
    MARINUCCI, M
    TENTORI, L
    FONTANAROSA, PP
    ROSSI, U
    BIAGIOTTI, S
    HEMOGLOBIN, 1978, 2 (03) : 249 - 259