ENZYMATIC STUDIES OF URINARY ISOMERIC CHONDROITIN SULFATES FROM PATIENTS WITH MUCOPOLYSACCHARIDOSES - THE APPLICATION OF HIGH-PERFORMANCE LIQUID-CHROMATOGRAPHY

被引:24
作者
LEE, GJL
EVANS, JE
TIECKELMANN, H
DULANEY, JT
NAYLOR, EW
机构
[1] SUNY BUFFALO,DEPT CHEM,BUFFALO,NY 14214
[2] SUNY BUFFALO,DEPT PEDIAT,BUFFALO,NY 14214
[3] UNIV TENNESSEE,CTR HLTH SCI,DEPT NEPHROL,MEMPHIS,TN 38163
关键词
D O I
10.1016/0009-8981(80)90135-7
中图分类号
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号
1001 ;
摘要
引用
收藏
页码:65 / 75
页数:11
相关论文
共 33 条
[1]   ANALYSIS OF URINARY MUCOPOLYSACCHARIDES USING SMALL ION-EXCHANGE COLUMNS [J].
APPLEGARTH, DA ;
BOZOIAN, G ;
LOWRY, RB .
CLINICAL BIOCHEMISTRY, 1975, 8 (03) :151-160
[2]   A MODIFIED URONIC ACID CARBAZOLE REACTION [J].
BITTER, T ;
MUIR, HM .
ANALYTICAL BIOCHEMISTRY, 1962, 4 (04) :330-&
[3]   DIFFERENTIATION OF MUCOPOLYSACCHARIDOSES BY ANALYSES OF EXCRETED SULFATED MUCOPOLYSACCHARIDES [J].
COHEN, DM ;
MOURAO, PAS ;
DIETRICH, CP .
CLINICA CHIMICA ACTA, 1977, 80 (03) :555-562
[4]   DIFFERENTIATION OF HUNTERS AND HURLERS SYNDROMES BY ANALYSIS OF EXCRETED MUCOPOLYSACCHARIDES [J].
DIETRICH, CP ;
NADER, HB ;
MOURAO, PAS .
BIOCHEMICAL MEDICINE, 1973, 8 (03) :371-379
[5]   IDENTIFICATION OF ACIDIC MUCOPOLYSACCHARIDES BY AGAROSE-GEL ELECTROPHORESIS [J].
DIETRICH, CP ;
MCDUFFIE, NM ;
SAMPAIO, LO .
JOURNAL OF CHROMATOGRAPHY, 1977, 130 (JAN11) :299-304
[6]   MUCOPOLYSACCHARIDOSES [J].
DORFMAN, A ;
MATALON, R .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1976, 73 (02) :630-637
[7]   MICRO-ASSAY OF DISACCHARIDE ISOMERS OF CHONDROITIN SULFATE [J].
ELLIOTT, RJ ;
GARDNER, DL .
BIOCHIMICA ET BIOPHYSICA ACTA, 1977, 498 (02) :349-354
[8]  
FRANSSON LA, 1968, J BIOL CHEM, V243, P1504
[9]   MICRO COLORIMETRIC DETERMINATION OF ACIDIC GLYCOSAMINOGLYCANS BY 2-DIMENSIONAL ELECTROPHORESIS ON A CELLULOSE-ACETATE STRIP [J].
HATA, R ;
NAGAI, Y .
ANALYTICAL BIOCHEMISTRY, 1973, 52 (02) :652-656
[10]   ACRYLAMIDE GEL ELECTROPHORESIS OF ACIDIC MUCOPOLYSACCHARIDES [J].
HILBORN, JC ;
ANASTASSIADIS, PA .
ANALYTICAL BIOCHEMISTRY, 1969, 31 (1-3) :51-+