Management of Localized Ovarian Juvenile Granulosa Cell Tumor with Ascites: case report

Background: Juvenile Granulosa Cell Tumor (JGCT) is a rare neoplasm in children. The clinical presentation usually includes a painful abdominal mass and pseudo-precocious puberty. The mainstay of treatment is surgical salpingo-oophorectomy for all cases, followed by platinum containing chemotherapy in advanced cases. Case Report: We present a case of JGCT in a 2-year-old girl who presented with a history of precocious puberty for 1 year. The imaging studies showed an left ovary mass measuring 5.0. A laparotomy identifi ed peritoneal fl uid and a tumor of the left ovary. Before the manipulation of the tumor, a sample of the peritoneal fl uid was collected followed by a left salpingooophorectomy. The analysis of the peritoneal fl uid identifi ed neoplasic cells. The patient then received chemotherapy with cisplatinum, etoposide and ifosfamide. Conclusions: This case emphasizes the importance of the peritoneal fl uid sampling before salpingooophorectomy allowing correct surgical staging and treatment decision.