MR IMAGING OF EARLY FIBRODYSPLASIA OSSIFICANS PROGRESSIVA

被引:13
作者
CARON, KH
DIPIETRO, MA
AISEN, AM
HEIDELBERGER, KP
PHILLIPS, WA
MARTEL, W
机构
[1] UNIV MICHIGAN HOSP,DEPT RADIOL,ANN ARBOR,MI 48109
[2] UNIV MICHIGAN HOSP,DEPT PATHOL,ANN ARBOR,MI 48109
[3] UNIV MICHIGAN HOSP,DEPT SURG,ORTHOPED SECT,ANN ARBOR,MI 48109
关键词
Anomalies; congenital; Children; Diseases; hereditary; Fibrodysplasia ossificans Progressiva; Magnetic resonance imaging;
D O I
10.1097/00004728-199003000-00035
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 ; 100207 ; 1009 ;
摘要
Fibrodysplasia ossificans progressiva is a rare disorder characterized by progressive heterotopic bone formation in connective tissue and muscle in association with congenital skeletal anomalies. The disease usually leads to extensive immobility and eventual disability. We report the magnetic resonance findings in a boy prior to ossification of his soft tissue masses. © 1990 Raven Press, ltd., New York.
引用
收藏
页码:318 / 321
页数:4
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