EVOLUTION OF CARDIOPULMONARY INVOLVEMENT IN FRIEDREICHS ATAXIA

被引：10

作者：

COTE, M ^{[1
]}

BUREAU, M ^{[1
]}

LEGER, C ^{[1
]}

MARTIN, J ^{[1
]}

GATTIKER, H ^{[1
]}

CIMON, M ^{[1
]}

LAROSE, A ^{[1
]}

LEMIEUX, B ^{[1
]}

机构：

[1] CTR HOSP UNIV SHERBROOKE,SHERBROOKE J1H 5N4,QUEBEC,CANADA

来源：

CANADIAN JOURNAL OF NEUROLOGICAL SCIENCES | 1979年 / 6卷 / 02期

关键词：

D O I：

10.1017/S0317167100119560

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

The evolution of 15patients initially evaluated during Phase One of the Quebec Cooperative Study of Friedreich's ataxia has been studied approximately three years later. It is concluded that the deterioration of cardio-pulmonary function in Friedreich's ataxia is multi-factorial. The neuromyopathy (or the underlying metabolic or cellular defect) appears to be the main contributing factor to the deterioration of cardio-pulmonary function, which is exacerbated by the scoliosis and varying severity of the cardiomyopathy. © 1979, Canadian Neurological Sciences Federation. All rights reserved.

引用

页码：151 / 157

页数：7

共 10 条

[1]

BUREAU M A, 1976, Canadian Journal of Neurological Sciences, V3, P343

[2]

Cobb JR., 1948, AM ACAD ORTHOP SURG, V5, P261

[3]

FERGUSON AB, 1945, ROENTGEN DIAGNOSIS E, P261

[4]

GEOFFROY G, 1976, Canadian Journal of Neurological Sciences, V3, P279

[5] PROSPECTS AND PREDICTIONS FOR CARDIOMYOPATHIES [J].

GOODWIN, JF .

CIRCULATION, 1974, 50 (02) :210-219

[6] SPINAL DEFORMITY ASSOCIATED WITH HERITABLE NEUROLOGICAL CONDITIONS - SPINAL MUSCULAR-ATROPHY, FRIEDREICHS ATAXIA, FAMILIAL DYSAUTONOMIA, AND CHARCOT-MARIE-TOOTH DISEASE [J].

HENSINGER, RN ;

MACEWEN, GD .

JOURNAL OF BONE AND JOINT SURGERY-AMERICAN VOLUME, 1976, 58 (01) :13-24

[7]

SANCHEZ-CASIS G, 1976, Canadian Journal of Neurological Sciences, V3, P349

[8]

THOREN C, 1964, ACTA PAEDIATRICA S

[9]

WENG TR, 1969, AM REV RESPIR DIS, V99, P879

[10]

1976, CAN J NEURO SCI, V3, P319

← 1 →