TRANSPORT OF LYSOSOMAL ENZYMES

被引:175
作者
NEUFELD, EF [1 ]
SANDO, GN [1 ]
GARVIN, AJ [1 ]
ROME, LH [1 ]
机构
[1] NIAMDD,BETHESDA,MD 20014
来源
JOURNAL OF SUPRAMOLECULAR STRUCTURE | 1977年 / 6卷 / 01期
关键词
D O I
10.1002/jss.400060108
中图分类号
O6 [化学];
学科分类号
0703 ;
摘要
引用
收藏
页码:95 / 101
页数:7
相关论文
共 47 条
[1]  
ACHORD D, IN PRESS
[2]  
ACHORD DT, 1977, FED PROC, V36, P653
[3]  
ASHWELL G, 1974, ADV ENZYMOL RAMB, V41, P99
[4]   DEFECT IN HURLER AND SCHEIE SYNDROMES - DEFICIENCY OF ALPHA-IDURONIDASE [J].
BACH, G ;
WEISSMAN.B ;
FRIEDMAN, R ;
NEUFELD, EF .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1972, 69 (08) :2048-&
[5]   IN-VITRO CORRECTION OF DEFICIENT HUMAN FIBROBLASTS BY BETA-GLUCURONIDASE FROM DIFFERENT HUMAN SOURCES [J].
BROT, FE ;
GLASER, JH ;
ROOZEN, KJ ;
SLY, WS .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1974, 57 (01) :1-8
[6]  
COHN ZA, 1969, LYSOSOMES BIOLOGY PA, V1, P44
[7]   FUNCTIONS OF LYSOSOMES [J].
DEDUVE, C ;
WATTIAUX, R .
ANNUAL REVIEW OF PHYSIOLOGY, 1966, 28 :435-+
[8]  
DINGLE JT, 1969, LYSOSOMES BIOLOGY PA, V2, P420
[9]   SOLITARY CELLS AND ENZYME EXCHANGE IN TETRAPARENTAL MICE [J].
FEDER, N .
NATURE, 1976, 263 (5572) :67-69
[10]  
FRANKEL HA, IN PRESS