ADRENOMYELONEUROPATHY - INCREASED ACCUMULATION OF VERY LONG-CHAIN FATTY-ACID IN CULTURED SKELETAL-MUSCLE

被引:10
作者
MCLAUGHLIN, J
ASKANAS, V
ENGEL, WK
机构
关键词
D O I
10.1016/0006-291X(80)90414-3
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:1202 / 1207
页数:6
相关论文
共 17 条
[1]   TECHNIQUE OF FIBER SELECTION FROM HUMAN MUSCLE-TISSUE CULTURES FOR HISTOCHEMICAL-ELECTRONMICROSCOPIC STUDIES [J].
ASKANAS, V ;
ENGEL, WK .
JOURNAL OF HISTOCHEMISTRY & CYTOCHEMISTRY, 1975, 23 (02) :144-146
[2]   ABNORMALITIES IN CULTURED MUSCLE AND PERIPHERAL-NERVE OF A PATIENT WITH ADRENOMYELONEUROPATHY [J].
ASKANAS, V ;
MCLAUGHLIN, J ;
ENGEL, WK ;
ADORNATO, BT .
NEW ENGLAND JOURNAL OF MEDICINE, 1979, 301 (11) :588-590
[3]   NEW PROGRAM FOR INVESTIGATING ADULT HUMAN SKELETAL-MUSCLE GROWN ANEURALLY IN TISSUE-CULTURE [J].
ASKANAS, V ;
ENGEL, WK .
NEUROLOGY, 1975, 25 (01) :58-67
[4]  
BAILEY JM, 1977, LIPID METABOLISM MAM, V2, P323
[5]   ADRENOMYELONEUROPATHY - PROBABLE VARIANT OF ADRENOLEUKODYSTROPHY .1. CLINICAL AND ENDOCRINOLOGIC ASPECTS [J].
GRIFFIN, JW ;
GOREN, E ;
SCHAUMBURG, H ;
ENGEL, WK ;
LORIAUX, L .
NEUROLOGY, 1977, 27 (12) :1107-1113
[6]  
Howard B V, 1974, Adv Lipid Res, V12, P51
[7]   FATTY-ACID ABNORMALITY IN ADRENOLEUKODYSTROPHY [J].
IGARASHI, M ;
SCHAUMBURG, HH ;
POWERS, J ;
KISHIMOTO, Y ;
KOLODNY, E ;
SUZUKI, K .
JOURNAL OF NEUROCHEMISTRY, 1976, 26 (04) :851-&
[8]   HIGH-CONCENTRATION OF HEXACOSANOATE IN CULTURED SKIN FIBROBLAST LIPIDS FROM ADRENOLEUKODYSTROPHY PATIENTS [J].
KAWAMURA, N ;
MOSER, AB ;
MOSER, HW ;
OGINO, T ;
SUZUKI, K ;
SCHAUMBURG, H ;
MILUNSKY, A ;
MURPHY, J ;
KISHIMOTO, Y .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1978, 82 (01) :114-120
[9]  
LOWRY OH, 1951, J BIOL CHEM, V193, P265
[10]   LIPID-COMPOSITION OF ERYTHROCYTES - FINDINGS IN DUCHENNES MUSCULAR-DYSTROPHY AND MYOTONIC ATROPHY [J].
MCLAUGHLIN, J ;
ENGEL, WK .
ARCHIVES OF NEUROLOGY, 1979, 36 (06) :351-354