FRIEDREICHS ATAXIA IN NORTHERN ITALY .2. BIOCHEMICAL-STUDIES IN CULTURED-CELLS

被引：8

作者：

BERTAGNOLIO, B

UZIEL, G

BOTTACHI, E

CRENNA, G

DANGELO, A

DIDONATO, S

机构：

来源：

CANADIAN JOURNAL OF NEUROLOGICAL SCIENCES | 1980年 / 7卷 / 04期

关键词：

D O I：

10.1017/S0317167100022964

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

引用

页码：409 / 412

页数：4

共 14 条

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[6]

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[7] PYRUVATE-DEHYDROGENASE DEFICIENCY IN SPINOCEREBELLAR DEGENERATIONS [J].

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RODRIGUEZBUDELLI, M .

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[8]

LOWRY OH, 1951, J BIOL CHEM, V193, P265

[9] PYRUVATE-DEHYDROGENASE, LIPOAMIDE DEHYDROGENASE AND CITRATE SYNTHASE ACTIVITY IN FIBROBLASTS FROM PATIENTS WITH FRIEDREICH AND CHARLEVOIX-SAGUENAY ATAXIA [J].

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[10]

PLAITAKIS A, 1979, ANN NEUROL, V6, P148

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