Newly Diagnosed Familial Alveolar Microlithiasis (Case Report of Two Brothers)

被引:0
作者
Okutan, Oguzhan [1 ]
Kartaloglu, Zafer [1 ]
Ilvan, Ahmet [1 ]
Bozkanat, Erkan [1 ]
Demirer, Ersin [1 ]
Silit, Emir [2 ]
Yildirim, Sukru [3 ]
Narin, Yavuz [4 ]
机构
[1] Gulhane Askeri Tip Akad Haydarpasa, Gogus Hastaliklari, Istanbul, Turkey
[2] Gulhane Askeri Tip Akad Haydarpasa, Radyol, Istanbul, Turkey
[3] Gulhane Askeri Tip Akad Haydarpasa, Patol, Istanbul, Turkey
[4] Gulhane Askeri Tip Akad Haydarpasa, Nukl Tip, Istanbul, Turkey
关键词
pulmonary; microlithiasis; familial;
D O I
暂无
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
Pulmonary alveolar microlithiasis (PAM) is a rare disease. It is progressive characterized with deposition of calcified granules in the alveolar space. Though etiology is not known, 50% of cases diagnosed have familial history. Our case was a 22-years-old soldier. During screening program, lesions on his chest roentgenogram were detected, he was admitted. His high resolution computerized tomography was compatible with PAM. Histologic diagnosis of the disease was provided by bronchoscopic biopsy. The bone scintigraphy supported the diagnosis. The patient's brother was also diagnosed PAM..
引用
收藏
页码:127 / 129
页数:3
相关论文
共 18 条
  • [1] PULMONARY ALVEOLAR MICROLITHIASIS - REPORT OF 5 CASES WITH SPECIAL REFERENCE TO ROENTGEN MANIFESTATIONS
    BALIKIAN, JP
    FULEIHAN, FJ
    NUCHO, CN
    [J]. AMERICAN JOURNAL OF ROENTGENOLOGY RADIUM THERAPY AND NUCLEAR MEDICINE, 1968, 103 (03): : 509 - &
  • [2] Caffrey PR, 1965, PEDIATRICS, V66, P758
  • [3] Caputi M, 1990, Arch Monaldi Mal Torace, V45, P353
  • [4] Pulmonary alveolar microlithiasis - World cases and review of the literature
    Castellana, G
    Lamorgese, V
    [J]. RESPIRATION, 2003, 70 (05) : 549 - 555
  • [5] Chang YC, 1999, J FORMOS MED ASSOC, V98, P440
  • [6] PULMONARY ALVEOLAR MICROLITHIASIS - CT FINDINGS
    CLUZEL, P
    GRENIER, P
    BERNADAC, P
    LAURENT, F
    PICARD, JD
    [J]. JOURNAL OF COMPUTER ASSISTED TOMOGRAPHY, 1991, 15 (06) : 938 - 942
  • [7] Corrin B, 2003, RESP MED, P1683
  • [8] PULMONARY ALVEOLAR MICROLITHIASIS - LUNG FUNCTION IN 5 CASES
    FULEIHAN, FJ
    ABBOUD, RT
    BALIKIAN, JP
    NUCHO, CKN
    [J]. THORAX, 1969, 24 (01) : 84 - &
  • [9] GOCMEN A, 1992, RESPIRATION, V59, P250
  • [10] Josman MC, 1957, AM J ROENTGENOL, V77, P947