EXCRETION OF ALPHA-KETO-DELTA-GUANIDINOVALERIC ACID AND ITS CYCLIC FORM IN PATIENTS WITH HYPERARGININEMIA

被引:10
作者
MARESCAU, B
PINTENS, J
LOWENTHAL, A
TERHEGGEN, HG
机构
关键词
D O I
10.1016/0009-8981(79)90162-1
中图分类号
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号
1001 ;
摘要
α-Keto-δ-guanidinovaleric acid, in equilibrium with its cyclic form, has been identified in the urines of three sisters affected with hyperargininemia. Identification was achieved on the basis of its similarity with the enzymatically synthesized compounds. © 1979.
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页码:35 / 38
页数:4
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共 8 条
  • [1] COOPER AJL, 1978, J BIOL CHEM, V253, P5407
  • [2] GAMMA-GUANIDINOBUTYRIC ACID AS A CONVULSIVE SUBSTANCE
    JINNAI, D
    SAWAI, A
    MORI, A
    [J]. NATURE, 1966, 212 (5062) : 617 - &
  • [3] JINNAI D, 1969, JAP J BRAIN PHYSL, V106, P3688
  • [4] MEISTER A, 1953, J BIOL CHEM, V200, P571
  • [5] Mizuno A., 1975, IRCS MED SCI, V3, P385
  • [6] SAKAGUCHI S, 1925, J BIOCHEM-TOKYO, V5, P133
  • [7] AUTOMATED TECHNIQUE FOR ANALYSIS OF PLASMA GUANIDINO ACIDS, AND SOME FINDINGS IN CHRONIC RENAL-DISEASE
    SHAINKIN, R
    BERKENSTADT, Y
    GIATT, Y
    BERLYNE, GM
    [J]. CLINICA CHIMICA ACTA, 1975, 60 (01) : 45 - 50
  • [8] WIECHERT P, 1976, J GENET HUM, V24, P61