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- [13] ALTERED KINETIC-PROPERTIES OF THE BRANCHED-CHAIN ALPHA-KETO ACID DEHYDROGENASE COMPLEX DUE TO MUTATION OF THE BETA-SUBUNIT OF THE BRANCHED-CHAIN ALPHA-KETO ACID DECARBOXYLASE (E1) COMPONENT IN LYMPHOBLASTOID-CELLS DERIVED FROM PATIENTS WITH MAPLE SYRUP URINE DISEASE JOURNAL OF CLINICAL INVESTIGATION, 1987, 80 (01) : 63 - 70
- [18] ISOLATION AND SEQUENCING OF A CDNA-ENCODING THE DECARBOXYLASE (E1)-ALPHA PRECURSOR OF BOVINE BRANCHED-CHAIN ALPHA-KETO ACID DEHYDROGENASE COMPLEX - EXPRESSION OF E1-ALPHA MESSENGER-RNA AND SUBUNIT IN MAPLE-SYRUP-URINE-DISEASE AND 3T3-L1 CELLS JOURNAL OF BIOLOGICAL CHEMISTRY, 1988, 263 (18) : 9007 - 9014