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FASTING HYPOGLYCEMIA RESULTING FROM HEPATIC CARNITINE PALMITOYL TRANSFERASE DEFICIENCY
被引:147
作者
:
BOUGNERES, PF
论文数:
0
引用数:
0
h-index:
0
BOUGNERES, PF
SAUDUBRAY, JM
论文数:
0
引用数:
0
h-index:
0
SAUDUBRAY, JM
MARSAC, C
论文数:
0
引用数:
0
h-index:
0
MARSAC, C
BERNARD, O
论文数:
0
引用数:
0
h-index:
0
BERNARD, O
ODIEVRE, M
论文数:
0
引用数:
0
h-index:
0
ODIEVRE, M
GIRARD, J
论文数:
0
引用数:
0
h-index:
0
GIRARD, J
机构
:
来源
:
JOURNAL OF PEDIATRICS
|
1981年
/ 98卷
/ 05期
关键词
:
D O I
:
10.1016/S0022-3476(81)80834-7
中图分类号
:
R72 [儿科学];
学科分类号
:
100202 ;
摘要
:
引用
收藏
页码:742 / 746
页数:5
相关论文
共 25 条
[1]
BAKER L, 1973, PEDIATR RES, V7, P385
[2]
DISORDER OF MUSCLE LIPID-METABOLISM AND MYOGLOBINURIA - ABSENCE OF CARNITINE PALMITYL TRANSFERASE
BANK, WJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN HOSP, DEPT MED, 3400 SPRUCE ST, PHILADELPHIA, PA 19104 USA
BANK, WJ
DIMAURO, S
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN HOSP, DEPT MED, 3400 SPRUCE ST, PHILADELPHIA, PA 19104 USA
DIMAURO, S
BONILLA, E
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN HOSP, DEPT MED, 3400 SPRUCE ST, PHILADELPHIA, PA 19104 USA
BONILLA, E
CAPUZZI, DM
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN HOSP, DEPT MED, 3400 SPRUCE ST, PHILADELPHIA, PA 19104 USA
CAPUZZI, DM
ROWLAND, LP
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN HOSP, DEPT MED, 3400 SPRUCE ST, PHILADELPHIA, PA 19104 USA
ROWLAND, LP
[J].
NEW ENGLAND JOURNAL OF MEDICINE,
1975,
292
(09)
: 443
-
449
[3]
MEASUREMENT OF TRUE GLUCOSE PRODUCTION-RATES IN INFANCY AND CHILDHOOD WITH 6,6-DIDEUTEROGLUCOSE
BIER, DM
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT MED, DIV METAB, ST LOUIS, MO 63110 USA
BIER, DM
LEAKE, RD
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT MED, DIV METAB, ST LOUIS, MO 63110 USA
LEAKE, RD
HAYMOND, MW
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT MED, DIV METAB, ST LOUIS, MO 63110 USA
HAYMOND, MW
ARNOLD, KJ
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT MED, DIV METAB, ST LOUIS, MO 63110 USA
ARNOLD, KJ
GRUENKE, LD
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT MED, DIV METAB, ST LOUIS, MO 63110 USA
GRUENKE, LD
SPERLING, MA
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT MED, DIV METAB, ST LOUIS, MO 63110 USA
SPERLING, MA
KIPNIS, DM
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT MED, DIV METAB, ST LOUIS, MO 63110 USA
KIPNIS, DM
[J].
DIABETES,
1977,
26
(11)
: 1016
-
1023
[4]
BOUGNERES PF, 1980, NEW ENGL J MED, V302, P123
[5]
BIOCHEMICAL AND PHYSIOLOGIC CONSEQUENCES OF CARNITINE PALMITYLTRANSFERASE DEFICIENCY
CARROLL, JE
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT PEDIAT,ST LOUIS,MO 63110
CARROLL, JE
BROOKE, MH
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT PEDIAT,ST LOUIS,MO 63110
BROOKE, MH
DEVIVO, DC
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT PEDIAT,ST LOUIS,MO 63110
DEVIVO, DC
KAISER, KK
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT PEDIAT,ST LOUIS,MO 63110
KAISER, KK
HAGBERG, JM
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT PEDIAT,ST LOUIS,MO 63110
HAGBERG, JM
[J].
MUSCLE & NERVE,
1978,
1
(02)
: 103
-
110
[6]
METHOD FOR DETERMINATION OF CARNITINE IN PICOMOLE RANGE
CEDERBLA.G
论文数:
0
引用数:
0
h-index:
0
CEDERBLA.G
LINDSTED.S
论文数:
0
引用数:
0
h-index:
0
LINDSTED.S
[J].
CLINICA CHIMICA ACTA,
1972,
37
(NMAR)
: 235
-
&
[7]
GLYCEMIC RESPONSE TO 24-HOUR FAST IN NORMAL CHILDREN .3. INFLUENCE OF AGE
CHAUSSAIN, JL
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PARIS 5, FAC COCHIN, CTR ETUD CROISSANCE & ENDOCRINOL ENFANT, F-75006 PARIS, FRANCE
UNIV PARIS 5, FAC COCHIN, CTR ETUD CROISSANCE & ENDOCRINOL ENFANT, F-75006 PARIS, FRANCE
CHAUSSAIN, JL
论文数:
引用数:
h-index:
机构:
GEORGES, P
CALZADA, L
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PARIS 5, FAC COCHIN, CTR ETUD CROISSANCE & ENDOCRINOL ENFANT, F-75006 PARIS, FRANCE
UNIV PARIS 5, FAC COCHIN, CTR ETUD CROISSANCE & ENDOCRINOL ENFANT, F-75006 PARIS, FRANCE
CALZADA, L
JOB, JC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PARIS 5, FAC COCHIN, CTR ETUD CROISSANCE & ENDOCRINOL ENFANT, F-75006 PARIS, FRANCE
UNIV PARIS 5, FAC COCHIN, CTR ETUD CROISSANCE & ENDOCRINOL ENFANT, F-75006 PARIS, FRANCE
JOB, JC
[J].
JOURNAL OF PEDIATRICS,
1977,
91
(05)
: 711
-
714
[8]
CARNITINE-PALMITYL-TRANSFERASE DEFICIENCY
CUMMING, WJK
论文数:
0
引用数:
0
h-index:
0
机构:
LEICESTER GEN HOSP,DEPT NEPHROL,LEICESTER,ENGLAND
CUMMING, WJK
HARDY, M
论文数:
0
引用数:
0
h-index:
0
机构:
LEICESTER GEN HOSP,DEPT NEPHROL,LEICESTER,ENGLAND
HARDY, M
HUDGSON, P
论文数:
0
引用数:
0
h-index:
0
机构:
LEICESTER GEN HOSP,DEPT NEPHROL,LEICESTER,ENGLAND
HUDGSON, P
WALLS, J
论文数:
0
引用数:
0
h-index:
0
机构:
LEICESTER GEN HOSP,DEPT NEPHROL,LEICESTER,ENGLAND
WALLS, J
[J].
JOURNAL OF THE NEUROLOGICAL SCIENCES,
1976,
30
(2-3)
: 247
-
258
[9]
RECURRENT HYPOGLYCEMIA ASSOCIATED WITH GLUTARIC ACIDURIA TYPE-II IN AN ADULT
DUSHEIKO, G
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
DUSHEIKO, G
KEW, MC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
KEW, MC
JOFFE, BI
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
JOFFE, BI
LEWIN, JR
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
LEWIN, JR
MANTAGOS, S
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
MANTAGOS, S
TANAKA, K
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
TANAKA, K
[J].
NEW ENGLAND JOURNAL OF MEDICINE,
1979,
301
(26)
: 1405
-
1409
[10]
A SKELETAL-MUSCLE DISORDER ASSOCIATED WITH INTERMITTENT SYMPTOMS AND A POSSIBLE DEFECT OF LIPID METABOLISM
ENGEL, WK
论文数:
0
引用数:
0
h-index:
0
ENGEL, WK
VICK, NA
论文数:
0
引用数:
0
h-index:
0
VICK, NA
GLUECK, CJ
论文数:
0
引用数:
0
h-index:
0
GLUECK, CJ
LEVY, RI
论文数:
0
引用数:
0
h-index:
0
LEVY, RI
[J].
NEW ENGLAND JOURNAL OF MEDICINE,
1970,
282
(13)
: 697
-
+
←
1
2
3
→
共 25 条
[1]
BAKER L, 1973, PEDIATR RES, V7, P385
[2]
DISORDER OF MUSCLE LIPID-METABOLISM AND MYOGLOBINURIA - ABSENCE OF CARNITINE PALMITYL TRANSFERASE
BANK, WJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN HOSP, DEPT MED, 3400 SPRUCE ST, PHILADELPHIA, PA 19104 USA
BANK, WJ
DIMAURO, S
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN HOSP, DEPT MED, 3400 SPRUCE ST, PHILADELPHIA, PA 19104 USA
DIMAURO, S
BONILLA, E
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN HOSP, DEPT MED, 3400 SPRUCE ST, PHILADELPHIA, PA 19104 USA
BONILLA, E
CAPUZZI, DM
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN HOSP, DEPT MED, 3400 SPRUCE ST, PHILADELPHIA, PA 19104 USA
CAPUZZI, DM
ROWLAND, LP
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN HOSP, DEPT MED, 3400 SPRUCE ST, PHILADELPHIA, PA 19104 USA
ROWLAND, LP
[J].
NEW ENGLAND JOURNAL OF MEDICINE,
1975,
292
(09)
: 443
-
449
[3]
MEASUREMENT OF TRUE GLUCOSE PRODUCTION-RATES IN INFANCY AND CHILDHOOD WITH 6,6-DIDEUTEROGLUCOSE
BIER, DM
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT MED, DIV METAB, ST LOUIS, MO 63110 USA
BIER, DM
LEAKE, RD
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT MED, DIV METAB, ST LOUIS, MO 63110 USA
LEAKE, RD
HAYMOND, MW
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT MED, DIV METAB, ST LOUIS, MO 63110 USA
HAYMOND, MW
ARNOLD, KJ
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT MED, DIV METAB, ST LOUIS, MO 63110 USA
ARNOLD, KJ
GRUENKE, LD
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT MED, DIV METAB, ST LOUIS, MO 63110 USA
GRUENKE, LD
SPERLING, MA
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT MED, DIV METAB, ST LOUIS, MO 63110 USA
SPERLING, MA
KIPNIS, DM
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT MED, DIV METAB, ST LOUIS, MO 63110 USA
KIPNIS, DM
[J].
DIABETES,
1977,
26
(11)
: 1016
-
1023
[4]
BOUGNERES PF, 1980, NEW ENGL J MED, V302, P123
[5]
BIOCHEMICAL AND PHYSIOLOGIC CONSEQUENCES OF CARNITINE PALMITYLTRANSFERASE DEFICIENCY
CARROLL, JE
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT PEDIAT,ST LOUIS,MO 63110
CARROLL, JE
BROOKE, MH
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT PEDIAT,ST LOUIS,MO 63110
BROOKE, MH
DEVIVO, DC
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT PEDIAT,ST LOUIS,MO 63110
DEVIVO, DC
KAISER, KK
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT PEDIAT,ST LOUIS,MO 63110
KAISER, KK
HAGBERG, JM
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV,SCH MED,DEPT PEDIAT,ST LOUIS,MO 63110
HAGBERG, JM
[J].
MUSCLE & NERVE,
1978,
1
(02)
: 103
-
110
[6]
METHOD FOR DETERMINATION OF CARNITINE IN PICOMOLE RANGE
CEDERBLA.G
论文数:
0
引用数:
0
h-index:
0
CEDERBLA.G
LINDSTED.S
论文数:
0
引用数:
0
h-index:
0
LINDSTED.S
[J].
CLINICA CHIMICA ACTA,
1972,
37
(NMAR)
: 235
-
&
[7]
GLYCEMIC RESPONSE TO 24-HOUR FAST IN NORMAL CHILDREN .3. INFLUENCE OF AGE
CHAUSSAIN, JL
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PARIS 5, FAC COCHIN, CTR ETUD CROISSANCE & ENDOCRINOL ENFANT, F-75006 PARIS, FRANCE
UNIV PARIS 5, FAC COCHIN, CTR ETUD CROISSANCE & ENDOCRINOL ENFANT, F-75006 PARIS, FRANCE
CHAUSSAIN, JL
论文数:
引用数:
h-index:
机构:
GEORGES, P
CALZADA, L
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PARIS 5, FAC COCHIN, CTR ETUD CROISSANCE & ENDOCRINOL ENFANT, F-75006 PARIS, FRANCE
UNIV PARIS 5, FAC COCHIN, CTR ETUD CROISSANCE & ENDOCRINOL ENFANT, F-75006 PARIS, FRANCE
CALZADA, L
JOB, JC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PARIS 5, FAC COCHIN, CTR ETUD CROISSANCE & ENDOCRINOL ENFANT, F-75006 PARIS, FRANCE
UNIV PARIS 5, FAC COCHIN, CTR ETUD CROISSANCE & ENDOCRINOL ENFANT, F-75006 PARIS, FRANCE
JOB, JC
[J].
JOURNAL OF PEDIATRICS,
1977,
91
(05)
: 711
-
714
[8]
CARNITINE-PALMITYL-TRANSFERASE DEFICIENCY
CUMMING, WJK
论文数:
0
引用数:
0
h-index:
0
机构:
LEICESTER GEN HOSP,DEPT NEPHROL,LEICESTER,ENGLAND
CUMMING, WJK
HARDY, M
论文数:
0
引用数:
0
h-index:
0
机构:
LEICESTER GEN HOSP,DEPT NEPHROL,LEICESTER,ENGLAND
HARDY, M
HUDGSON, P
论文数:
0
引用数:
0
h-index:
0
机构:
LEICESTER GEN HOSP,DEPT NEPHROL,LEICESTER,ENGLAND
HUDGSON, P
WALLS, J
论文数:
0
引用数:
0
h-index:
0
机构:
LEICESTER GEN HOSP,DEPT NEPHROL,LEICESTER,ENGLAND
WALLS, J
[J].
JOURNAL OF THE NEUROLOGICAL SCIENCES,
1976,
30
(2-3)
: 247
-
258
[9]
RECURRENT HYPOGLYCEMIA ASSOCIATED WITH GLUTARIC ACIDURIA TYPE-II IN AN ADULT
DUSHEIKO, G
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
DUSHEIKO, G
KEW, MC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
KEW, MC
JOFFE, BI
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
JOFFE, BI
LEWIN, JR
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
LEWIN, JR
MANTAGOS, S
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
MANTAGOS, S
TANAKA, K
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
TANAKA, K
[J].
NEW ENGLAND JOURNAL OF MEDICINE,
1979,
301
(26)
: 1405
-
1409
[10]
A SKELETAL-MUSCLE DISORDER ASSOCIATED WITH INTERMITTENT SYMPTOMS AND A POSSIBLE DEFECT OF LIPID METABOLISM
ENGEL, WK
论文数:
0
引用数:
0
h-index:
0
ENGEL, WK
VICK, NA
论文数:
0
引用数:
0
h-index:
0
VICK, NA
GLUECK, CJ
论文数:
0
引用数:
0
h-index:
0
GLUECK, CJ
LEVY, RI
论文数:
0
引用数:
0
h-index:
0
LEVY, RI
[J].
NEW ENGLAND JOURNAL OF MEDICINE,
1970,
282
(13)
: 697
-
+
←
1
2
3
→