SYNDROMATIC HEPATIC DUCTULAR HYPOPLASIA (ARTERIOHEPATIC DYSPLASIA) - A CLINICAL AND HEPATIC HISTOLOGIC-STUDY OF 3 PATIENTS

被引:34
作者
BERMAN, MD
ISHAK, KG
SCHAEFER, EJ
BARNES, S
JONES, EA
机构
[1] NIAMDD, DIGEST DIS BRANCH,LIVER UNIT,LIVER DIS SECT, BLDG 10,ROOM 4D52, BETHESDA, MD 20205 USA
[2] NHLBI, MOLEC DIS BRANCH, BETHESDA, MD 20205 USA
[3] ARMED FORCES INST PATHOL, DEPT HEPAT PATHOL, WASHINGTON, DC 20306 USA
[4] UNIV ALABAMA, DEPT GASTROENTEROL, BIRMINGHAM, AL 35233 USA
关键词
D O I
10.1007/BF01308096
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
引用
收藏
页码:485 / 497
页数:13
相关论文
共 30 条
[1]  
Alagille D, 1979, Prog Liver Dis, V6, P471
[2]   HEPATIC DUCTULAR HYPOPLASIA ASSOCIATED WITH CHARACTERISTIC FACIES, VERTEBRAL MALFORMATIONS, RETARDED PHYSICAL, MENTAL AND SEXUAL DEVELOPMENT, AND CARDIAC MURMUR [J].
ALAGILLE, D ;
ODIEVRE, M ;
GAUTIER, M ;
DOMMERGUES, JP .
JOURNAL OF PEDIATRICS, 1975, 86 (01) :63-71
[3]  
ALAGILLE D, 1979, NEONATAL HEPATITIS B, P177
[4]   SIMPLIFIED PROCEDURE FOR ISOLATION OF BILE-ACIDS FROM SERUM BASED ON A BATCH EXTRACTION WITH NONIONIC RESIN-AMBERLITE XAD-7 [J].
BARNES, S ;
CHITRANUKROH, A .
ANNALS OF CLINICAL BIOCHEMISTRY, 1977, 14 (JUL) :235-239
[5]   PHENOBARBITAL EFFECTS IN CHOLESTATIC LIVER-DISEASE [J].
BLOOMER, JR ;
BOYER, JL .
ANNALS OF INTERNAL MEDICINE, 1975, 82 (03) :310-317
[6]   STUDIES OF ETIOLOGY OF NEONATAL HEPATITIS AND BILIARY ATRESIA [J].
DANKS, DM ;
CAMPBELL, PE ;
JACK, I ;
ROGERS, J ;
SMITH, AL .
ARCHIVES OF DISEASE IN CHILDHOOD, 1977, 52 (05) :360-367
[7]  
EVANS J, 1978, GASTROENTEROLOGY, V75, P875
[8]   EFFICACY AND SAFETY OF LONG-TERM PHENOBARBITAL THERAPY OF FAMILIAL CHOLESTASIS [J].
GHENT, CN ;
BLOOMER, JR ;
HSIA, YE .
JOURNAL OF PEDIATRICS, 1978, 93 (01) :127-132
[9]  
GOLDFISCHER S, 1980, AM J PATHOL, V99, P715
[10]  
GREENWOOD RD, 1976, PEDIATRICS, V58, P243