REPLACEMENT THERAPY FOR ALPHA-1-ANTITRYPSIN DEFICIENCY ASSOCIATED WITH EMPHYSEMA

被引:556
作者
WEWERS, MD
CASOLARO, MA
SELLERS, SE
SWAYZE, SC
MCPHAUL, KM
WITTES, JT
CRYSTAL, RG
机构
[1] NHLBI, PULM BRANCH, BLDG 10, RM 6D03, BETHESDA, MD 20892 USA
[2] NHLBI, BIOMETR RES BRANCH, BETHESDA, MD 20892 USA
关键词
D O I
10.1056/NEJM198704233161704
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:1055 / 1062
页数:8
相关论文
共 63 条
[1]  
BEATTY K, 1980, J BIOL CHEM, V255, P3931
[2]  
BECKER W, 1968, Z KLIN CHEM KLIN BIO, V6, P113
[3]   SOME FORMAL APPROACHES TO ANALYSIS OF KINETIC DATA IN TERMS OF LINEAR COMPARTMENTAL SYSTEMS [J].
BERMAN, M ;
SHAHN, E ;
WEISS, MF .
BIOPHYSICAL JOURNAL, 1962, 2 (03) :289-&
[4]  
BRUCE RM, 1984, AM REV RESPIR DIS, V130, P386
[5]  
BURROWS B, 1983, AM REV RESPIR DIS, V127, pS42
[6]   STRUCTURE AND VARIATION OF HUMAN ALPHA-1-ANTITRYPSIN [J].
CARRELL, RW ;
JEPPSSON, JO ;
LAURELL, CB ;
BRENNAN, SO ;
OWEN, MC ;
VAUGHAN, L ;
BOSWELL, DR .
NATURE, 1982, 298 (5872) :329-334
[7]  
CARRELL RW, 1979, ESSAYS MEDICAL BIOCH, V4, P83
[8]   SENSITIVE SUBSTRATES FOR HUMAN-LEUKOCYTE AND PORCINE PANCREATIC ELASTASE - STUDY OF THE MERITS OF VARIOUS CHROMOPHORIC AND FLUOROGENIC LEAVING GROUPS IN ASSAYS FOR SERINE PROTEASES [J].
CASTILLO, MJ ;
NAKAJIMA, K ;
ZIMMERMAN, M ;
POWERS, JC .
ANALYTICAL BIOCHEMISTRY, 1979, 99 (01) :53-64
[9]   PREPARATION AND PROPERTIES OF ALPHA-1-PROTEINASE INHIBITOR CONCENTRATE FROM HUMAN-PLASMA [J].
COAN, MH ;
BROCKWAY, WJ ;
EGUIZABAL, H ;
KRIEG, T ;
FOURNEL, M .
VOX SANGUINIS, 1985, 48 (06) :333-342
[10]   PIM4 - AN ADDITIONAL PIM SUBTYPE [J].
CONSTANS, J ;
VIAU, M ;
GOUAILLARD, C .
HUMAN GENETICS, 1980, 55 (01) :119-121